{"id":281,"date":"2026-01-21T15:36:43","date_gmt":"2026-01-21T13:36:43","guid":{"rendered":"https:\/\/www.ipsen.com\/poland\/?page_id=281"},"modified":"2026-02-19T15:31:24","modified_gmt":"2026-02-19T13:31:24","slug":"rzadkie-cholestatyczne-choroby-watroby","status":"publish","type":"page","link":"https:\/\/www.ipsen.com\/poland\/choroby-rzadkie\/rzadkie-cholestatyczne-choroby-watroby\/","title":{"rendered":"Rzadkie cholestatyczne choroby w\u0105troby"},"content":{"rendered":"    <section class=\"sub-page-banner bg-color-enabled  banner-no-filter\" style=\"background: linear-gradient(93.64deg, #224A81 2.99%, #2797D3 97.01%)\">\n                <div class=\"container content-sec\">\n            <nav aria-label=\"breadcrumb\">\n            <ol class=\"breadcrumb\">\n                <li class=\"breadcrumb-item\"><a href=\"https:\/\/www.ipsen.com\/poland\">Strona g\u0142\u00f3wna<\/a><\/li><li class=\"breadcrumb-item visible\"><a href=\"https:\/\/www.ipsen.com\/poland\/choroby-rzadkie\/\">Choroby rzadkie<\/a><\/li><li class=\"breadcrumb-item active\"><a class=\"link-pointer-events-none\" href=\"#\" aria-current=\"page\">Rzadkie cholestatyczne choroby w\u0105troby<\/a><\/li><\/ol>\n            <\/nav>            <h1 class=\"visible banner-font-color-white\">Rzadkie cholestatyczne choroby w\u0105troby<\/h1>\n            <p class=\"hidden banner-font-color-white\"><\/p>\n        <\/div>\n    <\/section>\n\n\n\n\n<section class=\"media-tabs\">\n      <div class=\"container\">\n        <div class=\"media-tabs-inner\">\n          <ul class=\"media-list-ul\">\n                              <li class=\"media-list-items\">\n                      <a class=\"media-item-link \" href=\"https:\/\/www.ipsen.com\/poland\/choroby-rzadkie\/\">Choroby rzadkie<\/a>\n                  <\/li>\n                              <li class=\"media-list-items\">\n                      <a class=\"media-item-link active\" href=\"https:\/\/www.ipsen.com\/poland\/choroby-rzadkie\/rzadkie-cholestatyczne-choroby-watroby\/\">Rzadkie cholestatyczne choroby w\u0105troby<\/a>\n                  <\/li>\n                              <li class=\"media-list-items\">\n                      <a class=\"media-item-link \" href=\"https:\/\/www.ipsen.com\/poland\/choroby-rzadkie\/endokrynologiczne-zaburzenia-wzrostu\/\">Endokrynologiczne zaburzenia wzrostu<\/a>\n                  <\/li>\n                      <\/ul>\n          <div id=\"navTabArrows\">\n              <div class=\"tab-nav-arrows\" id=\"tab-nav-prev\"><\/div>\n              <div class=\"tab-nav-arrows\" id=\"tab-nav-next\"><\/div>\n          <\/div>\n        <\/div>\n      <\/div>\n<\/section>\n\n    <section class=\"title-text \">\n        <div class=\"container\">\n            <div class=\"title-text-inner\" style=\"background-color:#EDEBE4;\">\n\n                <!-- If heading is enabled then it's visible -->\n                <div class=\"text-head-dash hidden\">\n                <h3 class=\"heading-three\" role=\"heading\" aria-level=\"2\">\n                                            <\/h3>\n                <\/div>\n               \n                <!-- If description is enabled then it's visible -->\n                <div class=\"text-parbase visible\">\n                    <p>Rzadkie cholestatyczne choroby w\u0105troby to grupa schorze\u0144 atakuj\u0105cych drogi \u017c\u00f3\u0142ciowe, co prowadzi do post\u0119puj\u0105cego uszkodzenia w\u0105troby oraz objaw\u00f3w takich jak wyniszczaj\u0105ce zm\u0119czenie i uporczywy \u015bwi\u0105d sk\u00f3ry. Symptomy te, cho\u0107 cz\u0119sto niewidoczne i niezrozumia\u0142e, drastycznie obni\u017caj\u0105 jako\u015b\u0107 \u017cycia. Ze wzgl\u0119du na rzadko\u015b\u0107 tych chor\u00f3b, opcje terapeutyczne s\u0105 ograniczone, a pacjenci ka\u017cdego dnia mierz\u0105 si\u0119 z niezliczonymi wyzwaniami. Droga do diagnozy jest cz\u0119sto d\u0142uga i kr\u0119ta, pozostawiaj\u0105c chorych w poczuciu osamotnienia, niezrozumienia, a niekiedy nawet stygmatyzacji. Potrzeba innowacji w tym obszarze jest ogromna.<\/p>\n<p>Dostarczamy prze\u0142omowe terapie osobom \u017cyj\u0105cym z rzadkimi chorobami w\u0105troby. Posiadaj\u0105c ju\u017c 3 leki zatwierdzone w trzech rzadkich wskazaniach cholestatycznych, realizujemy t\u0119 misj\u0119, jednocze\u015bnie stale rozwijaj\u0105c nasze wiod\u0105ce w bran\u017cy portfolio projekt\u00f3w badawczych. Tworzenie lek\u00f3w zaczynamy od s\u0142uchania tych, kt\u00f3rzy \u017cyj\u0105 z chorob\u0105, ich rodzin oraz ekspert\u00f3w medycznych. Tylko w ten spos\u00f3b mo\u017cemy mie\u0107 pewno\u015b\u0107, \u017ce prawdziwe wyzwania pacjent\u00f3w s\u0105 zrozumiane i odzwierciedlone w projektach naszych bada\u0144 klinicznych, inicjatywach edukacyjnych i programach wsparcia.<\/p>\n                <\/div>\n\n                <!-- If button is enabled then it's visible -->\n                \n            <\/div>\n        <\/div>\n    <\/section>\n\n\n<!--Graphics Cards Carousel Start Here-->\n\n    <section class=\"graphic-card graphics-old-layout bg-color-disabled bg-image-disabled bg-video-disabled bg-mobile-video-img-disabled\"    data-displaycards=\"3\">\n                <div class=\"container\">\n            <div class=\"text-graph-inner\">\n                <div class=\"row\">\n                    <!--Graphic info section-->\n                    <div class=\"column-1 col-xl-12 col-md-12 col-sm-12\">\n                        <div class=\"text-graph-heading\">\n                        <h3 class=\"charcoal-grey hidden heading-three\" role=\"heading\" aria-level=\"2\">\n                                                            <\/h3>\n                            <p class=\"text-graph-para charcoal-grey hidden\"><\/p>\n                        <\/div>\n                    <\/div><!--Graphic info section over here -->\n\n                    <!--Graphic detail section-->\n                    <div class=\"column-2 col-xl-12 col-md-12 col-sm-12\">\n                        <!-- graphic-card carousel start here -->\n                                                    <div class=\"text-graph-carousel\">\n                                <div class=\"glider-contain multiple\">\n                                    \n                                <div class=\"glider-graphic-card\" tabindex=\"-1\">\n                                                                                                                        <div class=\"text-graphic\">\n                                                    <div class=\"text-graph-row\">\n                                                        \n                                                                <!-- Graphic Card With OLD layout start here -->\n                                                                <div class=\"column-1\">\n                                                                                                                                                <div class=\"text-graph-img visible graphic-icon-enabled \">\n                                                                                                                                                                    <img decoding=\"async\" src=\"https:\/\/www.ipsen.com\/poland\/wp-content\/uploads\/sites\/30\/2026\/01\/Medicine.png\" alt=\"\" \/> \n                                                                                                                                                            <\/div>\n                                                                                                                                    <\/div>\n                                                                <div class=\"column-2\">\n                                                                    <div class=\"text-graph-content\">\n                                                                                                                                                        <div class=\"text-graph-title\">\n                                                                                <h4 role=\"heading\" aria-level=\"3\">Potrzeba innowacji<\/h4>\n                                                                                <\/div>\n                                                                                                                                                <div class=\"text-graph-desc\">\n                                                                            <p><p>Istnieje co najmniej 20 r\u00f3\u017cnych rzadkich chor\u00f3b w\u0105troby, a ka\u017cda z nich jest unikalna.<\/p>\n<\/p>\n                                                                        <\/div>\n                                                                    <\/div>\n                                                                <\/div>\n                                                                <!-- Graphic Card With OLD layout end here -->\n                                                        \n                                                    <\/div>\n                                                <\/div>\n                                                                                                                                                                    <div class=\"text-graphic\">\n                                                    <div class=\"text-graph-row\">\n                                                        \n                                                                <!-- Graphic Card With OLD layout start here -->\n                                                                <div class=\"column-1\">\n                                                                                                                                                <div class=\"text-graph-img visible graphic-icon-enabled \">\n                                                                                                                                                                    <img decoding=\"async\" src=\"https:\/\/www.ipsen.com\/poland\/wp-content\/uploads\/sites\/30\/2026\/01\/Rare-Disease-Common.png\" alt=\"\" \/> \n                                                                                                                                                            <\/div>\n                                                                                                                                    <\/div>\n                                                                <div class=\"column-2\">\n                                                                    <div class=\"text-graph-content\">\n                                                                                                                                                        <div class=\"text-graph-title\">\n                                                                                <h4 role=\"heading\" aria-level=\"3\">Obci\u0105\u017cenie rzadkimi chorobami w\u0105troby<\/h4>\n                                                                                <\/div>\n                                                                                                                                                <div class=\"text-graph-desc\">\n                                                                            <p><p>Rzadkie choroby w\u0105troby wyst\u0119puj\u0105 cz\u0119\u015bciej, ni\u017c mog\u0142oby si\u0119 wydawa\u0107 \u2014 szacuje si\u0119, \u017ce dotykaj\u0105 1 na 50 000\u2013100 000 os\u00f3b.<\/p>\n<\/p>\n                                                                        <\/div>\n                                                                    <\/div>\n                                                                <\/div>\n                                                                <!-- Graphic Card With OLD layout end here -->\n                                                        \n                                                    <\/div>\n                                                <\/div>\n                                                                                                                                                                    <div class=\"text-graphic\">\n                                                    <div class=\"text-graph-row\">\n                                                        \n                                                                <!-- Graphic Card With OLD layout start here -->\n                                                                <div class=\"column-1\">\n                                                                                                                                                <div class=\"text-graph-img visible graphic-icon-enabled \">\n                                                                                                                                                                    <img decoding=\"async\" src=\"https:\/\/www.ipsen.com\/poland\/wp-content\/uploads\/sites\/30\/2026\/01\/Question-Marks.png\" alt=\"\" \/> \n                                                                                                                                                            <\/div>\n                                                                                                                                    <\/div>\n                                                                <div class=\"column-2\">\n                                                                    <div class=\"text-graph-content\">\n                                                                                                                                                        <div class=\"text-graph-title\">\n                                                                                <h4 role=\"heading\" aria-level=\"3\">Ograniczone zasoby wiedzy lub brak wiedzy<\/h4>\n                                                                                <\/div>\n                                                                                                                                                <div class=\"text-graph-desc\">\n                                                                            <p><p>Wi\u0119kszo\u015b\u0107 pracownik\u00f3w ochrony zdrowia posiada ograniczon\u0105 wiedz\u0119 na temat tych schorze\u0144 ze wzgl\u0119du na ich rzadko\u015b\u0107. Mo\u017ce to prowadzi\u0107 do op\u00f3\u017anionej diagnozy, obci\u0105\u017caj\u0105cych pacjent\u00f3w licznych bada\u0144 i wizyt, a tak\u017ce do kierowania chorych do niew\u0142a\u015bciwych specjalist\u00f3w, pr\u00f3buj\u0105c leczy\u0107 objawy.<\/p>\n<\/p>\n                                                                        <\/div>\n                                                                    <\/div>\n                                                                <\/div>\n                                                                <!-- Graphic Card With OLD layout end here -->\n                                                        \n                                                    <\/div>\n                                                <\/div>\n                                                                                                                <\/div>\n                            <\/div>\n                                            <\/div> <!-- graphic-card carousel end here -->\n                <\/div> <!--Graphic detail section over here with 12 grid -->   \n            <\/div><!--row ended here-->\n        <\/div> <!-- graph-inner ended here -->\n        \n            <div class=\"more-result-btn\">\n                                            <\/div>\n        <\/div> <!--Container class ended here -->\n    <\/section>\n<!--Graphics Cards Carousel End Here-->\n\n\n<!-- Text & Media Block Code -->\n<section class=\"two-col-section text-media-section\">\n    <div class=\"container two-section-innner \">\n        <div class=\"response-inner\" style=\"background-image: url('')\">\n            <div class=\"row \">\n                <div class=\"col-xs-12 col-sm-12 col-md-6\">\n                                                    <div class=\"img-video-section\">\n                                <img decoding=\"async\" \n                                    src=\"https:\/\/www.ipsen.com\/poland\/wp-content\/uploads\/sites\/30\/2026\/01\/cholestatic-2.jpg\" \n                                    alt=\"\" \n                                >\n                            <\/div>\n                                        <\/div>\n                <div class=\" col-xs-12 col-sm-12 col-md-6\">\n                    <div class=\"section-content\">\n                        <div class=\"heading-dash\">\n                                                            <span class=\"dash\"><\/span>\n                                <h4 class=\"heading-para heading-four\" role=\"heading\" aria-level=\"2\">\n                                    Pierwotne zapalenie dr\u00f3g \u017c\u00f3\u0142ciowych (PBC)                                <\/h4>\n                                                    <\/div>\n                                                <ul>\n<li>PBC jest rzadk\u0105, post\u0119puj\u0105c\u0105, autoimmunologiczn\u0105 cholestatyczn\u0105 chorob\u0105 w\u0105troby, w kt\u00f3rej dochodzi do nagromadzenia \u017c\u00f3\u0142ci i toksyn (cholestaza) oraz przewlek\u0142ego stanu zapalnego, prowadz\u0105cych do nieodwracalnego w\u0142\u00f3knienia (bliznowacenia) w\u0105troby oraz zniszczenia dr\u00f3g \u017c\u00f3\u0142ciowych.<\/li>\n<li>PBC dotyczy g\u0142\u00f3wnie kobiet w wieku od 40 do 60 lat.<\/li>\n<li>PBC jest schorzeniem przewlek\u0142ym, trwaj\u0105cym ca\u0142e \u017cycie, kt\u00f3re bez skutecznego leczenia mo\u017ce z czasem post\u0119powa\u0107, prowadz\u0105c do konieczno\u015bci przeszczepienia w\u0105troby, a w niekt\u00f3rych przypadkach do przedwczesnej \u015bmierci.<\/li>\n<li>PBC istotnie wp\u0142ywa na codzienne funkcjonowanie pacjent\u00f3w &#8211; osoby chore cz\u0119sto do\u015bwiadczaj\u0105 silnego zm\u0119czenia oraz wyniszczaj\u0105cego \u015bwi\u0105du sk\u00f3ry.<\/li>\n<\/ul>\n                            <a \n                            aria-label=\" about Pierwotne zapalenie dr\u00f3g \u017c\u00f3\u0142ciowych (PBC)\"  \n                                role=\"link\" \n                                class=\"btn-link hidden\"\n                                href=\"\" \n                                target=\"_self\"\n                            > \n                                 \n                            <\/a>\n\n                    <\/div>\n                <\/div>\n            <\/div>\n        <\/div>\n    <\/div>\n<\/section>\n\n<!-- Text & Media Block Code -->\n<section class=\"two-col-section text-media-section\">\n    <div class=\"container two-section-innner section-reverse\">\n        <div class=\"response-inner\" style=\"background-image: url('')\">\n            <div class=\"row section-reverse\">\n                <div class=\"col-xs-12 col-sm-12 col-md-6\">\n                                                    <div class=\"img-video-section\">\n                                <img decoding=\"async\" \n                                    src=\"https:\/\/www.ipsen.com\/poland\/wp-content\/uploads\/sites\/30\/2026\/01\/cholestatic-1.jpg\" \n                                    alt=\"\" \n                                >\n                            <\/div>\n                                        <\/div>\n                <div class=\" col-xs-12 col-sm-12 col-md-6\">\n                    <div class=\"section-content\">\n                        <div class=\"heading-dash\">\n                                                            <span class=\"dash\"><\/span>\n                                <h4 class=\"heading-para heading-four\" role=\"heading\" aria-level=\"2\">\n                                    Post\u0119puj\u0105ca rodzinna cholestaza wewn\u0105trzw\u0105trobowa (PFIC)                                <\/h4>\n                                                    <\/div>\n                                                <ul>\n<li>PFIC odnosi si\u0119 do grupy rzadkich chor\u00f3b genetycznych, w kt\u00f3rych w\u0105troba ma trudno\u015bci z prawid\u0142owym odprowadzaniem kwas\u00f3w \u017c\u00f3\u0142ciowych, co prowadzi do ich gromadzenia si\u0119 w w\u0105trobie, okre\u015blanego jako cholestaza wewn\u0105trzw\u0105trobowa.<\/li>\n<li>Chocia\u017c PFIC mo\u017ce ujawni\u0107 si\u0119 w wieku doros\u0142ym, zazwyczaj manifestuje si\u0119 i przebiega najci\u0119\u017cej u niemowl\u0105t oraz ma\u0142ych dzieci.<\/li>\n<li>PFIC mo\u017ce szybko post\u0119powa\u0107, prowadz\u0105c do marsko\u015bci w\u0105troby.<\/li>\n<li>Najbardziej wyniszczaj\u0105cym objawem PFIC jest \u015bwi\u0105d, kt\u00f3ry mo\u017ce by\u0107 tak nasilony, \u017ce doprowadza pacjent\u00f3w do uszkodze\u0144 sk\u00f3ry, zaburze\u0144 snu, dra\u017cliwo\u015bci, problem\u00f3w z koncentracj\u0105 oraz pogorszenia wynik\u00f3w nauce.<\/li>\n<li>Nawet do 80% pacjent\u00f3w cierpi z powodu \u015bwi\u0105du sk\u00f3ry.<\/li>\n<\/ul>\n                            <a \n                            aria-label=\" about Post\u0119puj\u0105ca rodzinna cholestaza wewn\u0105trzw\u0105trobowa (PFIC)\"  \n                                role=\"link\" \n                                class=\"btn-link hidden\"\n                                href=\"\" \n                                target=\"_self\"\n                            > \n                                 \n                            <\/a>\n\n                    <\/div>\n                <\/div>\n            <\/div>\n        <\/div>\n    <\/div>\n<\/section>\n\n<!-- Text & Media Block Code -->\n<section class=\"two-col-section text-media-section\">\n    <div class=\"container two-section-innner \">\n        <div class=\"response-inner\" style=\"background-image: url('')\">\n            <div class=\"row \">\n                <div class=\"col-xs-12 col-sm-12 col-md-6\">\n                                                    <div class=\"img-video-section\">\n                                <img decoding=\"async\" \n                                    src=\"https:\/\/www.ipsen.com\/poland\/wp-content\/uploads\/sites\/30\/2026\/01\/cholestatic-4.jpg\" \n                                    alt=\"\" \n                                >\n                            <\/div>\n                                        <\/div>\n                <div class=\" col-xs-12 col-sm-12 col-md-6\">\n                    <div class=\"section-content\">\n                        <div class=\"heading-dash\">\n                                                            <span class=\"dash\"><\/span>\n                                <h4 class=\"heading-para heading-four\" role=\"heading\" aria-level=\"2\">\n                                    Zesp\u00f3\u0142 Alagille\u2019a (ALGS)                                <\/h4>\n                                                    <\/div>\n                                                <ul>\n<li>ALGS jest rzadk\u0105, genetyczn\u0105 chorob\u0105 w\u0105troby, kt\u00f3ra dotyka g\u0142\u00f3wnie niemowl\u0119ta i ma\u0142e dzieci. W przebiegu choroby dochodzi do gromadzenia si\u0119 toksycznych kwas\u00f3w \u017c\u00f3\u0142ciowych na skutek zmniejszonej liczby, zw\u0119\u017cenia lub nieprawid\u0142owej budowy dr\u00f3g \u017c\u00f3\u0142ciowych.<\/li>\n<li>ALGS mo\u017ce zajmowa\u0107 wiele narz\u0105d\u00f3w w ca\u0142ym organizmie, w tym w\u0105trob\u0119, serce i nerki, a tak\u017ce powodowa\u0107 nieprawid\u0142owo\u015bci uk\u0142adu kostnego oraz oczu.<\/li>\n<li>Jednym z g\u0142\u00f3wnych objaw\u00f3w choroby jest uporczywy, trudny do opanowania \u015bwi\u0105d sk\u00f3ry, kt\u00f3ry mo\u017ce by\u0107 tak nasilony, \u017ce prowadzi do konieczno\u015bci przeszczepienia w\u0105troby.<\/li>\n<\/ul>\n                            <a \n                            aria-label=\" about Zesp\u00f3\u0142 Alagille\u2019a (ALGS)\"  \n                                role=\"link\" \n                                class=\"btn-link hidden\"\n                                href=\"\" \n                                target=\"_self\"\n                            > \n                                 \n                            <\/a>\n\n                    <\/div>\n                <\/div>\n            <\/div>\n        <\/div>\n    <\/div>\n<\/section>\n\n\n<div class=\"wp-block-group\"><div class=\"wp-block-group__inner-container is-layout-constrained wp-block-group-is-layout-constrained\">\n<h3 class=\"wp-block-heading\">Obszary badawczo &#8211; rozwojowe Ipsen w obszarze rzadkich chor\u00f3b w\u0105troby<\/h3>\n<\/div><\/div>\n\n\n<!-- Text & Media Block Code -->\n<section class=\"two-col-section text-media-section\">\n    <div class=\"container two-section-innner section-reverse\">\n        <div class=\"response-inner\" style=\"background-image: url('')\">\n            <div class=\"row section-reverse\">\n                <div class=\"col-xs-12 col-sm-12 col-md-6\">\n                                                    <div class=\"img-video-section\">\n                                <img decoding=\"async\" \n                                    src=\"https:\/\/www.ipsen.com\/poland\/wp-content\/uploads\/sites\/30\/2026\/01\/cholestatic-5-Edited-2.jpg\" \n                                    alt=\"\" \n                                >\n                            <\/div>\n                                        <\/div>\n                <div class=\" col-xs-12 col-sm-12 col-md-6\">\n                    <div class=\"section-content\">\n                        <div class=\"heading-dash\">\n                                                            <span class=\"dash\"><\/span>\n                                <h4 class=\"heading-para heading-four\" role=\"heading\" aria-level=\"2\">\n                                    Atrezja dr\u00f3g \u017c\u00f3\u0142ciowych (BA)                                <\/h4>\n                                                    <\/div>\n                                                <ul>\n<li>BA jest chorob\u0105 dotykaj\u0105c\u0105 dzieci, w kt\u00f3rej dochodzi do bliznowacenia i niedro\u017cno\u015bci dr\u00f3g \u017c\u00f3\u0142ciowych zar\u00f3wno wewn\u0105trz, jak i na zewn\u0105trz w\u0105troby.<\/li>\n<li>Poniewa\u017c \u017c\u00f3\u0142\u0107 nie mo\u017ce odp\u0142ywa\u0107 do jelit, gromadzi si\u0119 w w\u0105trobie, powoduj\u0105c jej uszkodzenie. Prowadzi to do w\u0142\u00f3knienia, utraty tkanki i funkcji w\u0105troby oraz rozwoju marsko\u015bci.<\/li>\n<\/ul>\n                            <a \n                            aria-label=\" about Atrezja dr\u00f3g \u017c\u00f3\u0142ciowych (BA)\"  \n                                role=\"link\" \n                                class=\"btn-link hidden\"\n                                href=\"\" \n                                target=\"_self\"\n                            > \n                                 \n                            <\/a>\n\n                    <\/div>\n                <\/div>\n            <\/div>\n        <\/div>\n    <\/div>\n<\/section>\n\n<!-- Text & Media Block Code -->\n<section class=\"two-col-section text-media-section\">\n    <div class=\"container two-section-innner \">\n        <div class=\"response-inner\" style=\"background-image: url('')\">\n            <div class=\"row \">\n                <div class=\"col-xs-12 col-sm-12 col-md-6\">\n                                                    <div class=\"img-video-section\">\n                                <img decoding=\"async\" \n                                    src=\"https:\/\/www.ipsen.com\/poland\/wp-content\/uploads\/sites\/30\/2026\/01\/cholestatic-3.jpg\" \n                                    alt=\"\" \n                                >\n                            <\/div>\n                                        <\/div>\n                <div class=\" col-xs-12 col-sm-12 col-md-6\">\n                    <div class=\"section-content\">\n                        <div class=\"heading-dash\">\n                                                            <span class=\"dash\"><\/span>\n                                <h4 class=\"heading-para heading-four\" role=\"heading\" aria-level=\"2\">\n                                    Pierwotne stwardniaj\u0105ce zapalenie dr\u00f3g \u017c\u00f3\u0142ciowych (PSC)                                <\/h4>\n                                                    <\/div>\n                                                <ul>\n<li>PSC jest rzadk\u0105 chorob\u0105 w\u0105troby o pod\u0142o\u017cu immunologicznym, w kt\u00f3rej stan zapalny i w\u0142\u00f3knienie (bliznowacenie) prowadz\u0105 do post\u0119puj\u0105cego twardnienia i zw\u0119\u017cania dr\u00f3g \u017c\u00f3\u0142ciowych zar\u00f3wno wewn\u0105trz, jak i na zewn\u0105trz w\u0105troby.<\/li>\n<li>Objawy mog\u0105 obejmowa\u0107 b\u00f3l brzucha, \u015bwi\u0105d sk\u00f3ry, biegunk\u0119, \u017c\u00f3\u0142taczk\u0119, zm\u0119czenie oraz uczucie os\u0142abienia.<\/li>\n<li>Wielu pacjent\u00f3w w momencie rozpoznania PSC nie wykazuje \u017cadnych objaw\u00f3w.<\/li>\n<li>U wielu chorych, w zaawansowanym stadium prowadz\u0105cym do niewydolno\u015bci w\u0105troby, jedyn\u0105 dost\u0119pn\u0105 opcj\u0105 leczenia pozostaje przeszczepienie w\u0105troby.<\/li>\n<\/ul>\n                            <a \n                            aria-label=\" about Pierwotne stwardniaj\u0105ce zapalenie dr\u00f3g \u017c\u00f3\u0142ciowych (PSC)\"  \n                                role=\"link\" \n                                class=\"btn-link hidden\"\n                                href=\"\" \n                                target=\"_self\"\n                            > \n                                 \n                            <\/a>\n\n                    <\/div>\n                <\/div>\n            <\/div>\n        <\/div>\n    <\/div>\n<\/section>","protected":false},"excerpt":{"rendered":"","protected":false},"author":2,"featured_media":0,"parent":88,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"_acf_changed":false,"footnotes":""},"class_list":["post-281","page","type-page","status-publish","hentry","entry"],"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v26.8 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Rzadkie cholestatyczne choroby w\u0105troby - 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