{"id":85888,"date":"2025-08-25T13:52:35","date_gmt":"2025-08-25T11:52:35","guid":{"rendered":"https:\/\/www.ipsen.com\/?p=85888"},"modified":"2025-08-25T13:51:59","modified_gmt":"2025-08-25T11:51:59","slug":"comprendre-la-cbp-gerer-lessentiel","status":"publish","type":"post","link":"https:\/\/www.ipsen.com\/fr\/actualites\/rare-diseases-fr\/comprendre-la-cbp-gerer-lessentiel\/","title":{"rendered":"Comprendre la CBP\u202f: G\u00e9rer l\u2019essentiel\u00a0"},"content":{"rendered":"\n<p>Sandra Silvestri, d\u2019Ipsen, a rencontr\u00e9 le Dr Laura Cristoferi, le Professeur Mark Swain et le Professeur David Jones pour explorer les derni\u00e8res donn\u00e9es probantes sur la prise en charge de la cholangite biliaire primitive (CBP), une maladie auto-immune rare. Lors de la discussion, les intervenants ont soulign\u00e9 l\u2019importance d\u2019approches de soins holistiques et individualis\u00e9es, ainsi que de permettre aux patients de jouer un r\u00f4le actif dans la prise en charge de leur maladie. Ils ont \u00e9galement \u00e9voqu\u00e9 la n\u00e9cessit\u00e9 de prendre en compte les sympt\u00f4mes les plus importants pour les patients afin d\u2019am\u00e9liorer leur pronostic et leur bien-\u00eatre g\u00e9n\u00e9ral.\u00a0<\/p>\n\n\n    <section class=\"video-card \">\n        <div class=\"container\">\n            <!-- Block Details -->\n            <div class=\"video-card-header\">\n                <h3 class=\"video-card-block-title hidden heading-three\">\n                                    <\/h3>\n                <p class=\"charcoal-grey video-card-block-summary hidden\"> \n                                    <\/p>\n            <\/div>\n\n            <!-- Video Iframe embed -->\n                            <div class=\"video-embed\"> \n                <iframe loading=\"lazy\" title=\"Video snippet 1\" src=\"https:\/\/player.vimeo.com\/video\/1112863099?app_id=122963&#038;autoplay=1&#038;muted=1&#038;controls=1&#038;loop=1&#038;autopause=1&#038;background=0\" width=\"640\" height=\"360\" frameborder=\"0\" allow=\"autoplay; fullscreen; picture-in-picture; clipboard-write; encrypted-media; web-share\" referrerpolicy=\"strict-origin-when-cross-origin\" frameborder=\"0\" allow=\"autoplay; fullscreen; picture-in-picture\" data-ot-ignore><\/iframe>                <\/div>\n            \n            <!-- Block CTA -->\n            <div class=\"cta-block hidden\">\n                            <\/div>\n\n        <\/div>\n    <\/section>\n\n\n\n<p>Le parcours de chaque personne atteinte de CBP est unique. Si ralentir la progression de la maladie est une priorit\u00e9, la gestion des sympt\u00f4mes est \u00e9galement primordiale pour les personnes atteintes de CBP, car ce sont souvent les aspects qui impactent le plus leur vie. Deux des sympt\u00f4mes les plus fr\u00e9quents chez les personnes atteintes de CBP sont la fatigue et le prurit (d\u00e9mangeaisons).\u00a0<\/p>\n\n\n    <section class=\"video-card \">\n        <div class=\"container\">\n            <!-- Block Details -->\n            <div class=\"video-card-header\">\n                <h3 class=\"video-card-block-title hidden heading-three\">\n                                    <\/h3>\n                <p class=\"charcoal-grey video-card-block-summary hidden\"> \n                                    <\/p>\n            <\/div>\n\n            <!-- Video Iframe embed -->\n                            <div class=\"video-embed\"> \n                <iframe loading=\"lazy\" title=\"Video snippet 2\" src=\"https:\/\/player.vimeo.com\/video\/1112862960?app_id=122963&#038;autoplay=1&#038;muted=1&#038;controls=1&#038;loop=1&#038;autopause=1&#038;background=0\" width=\"640\" height=\"360\" frameborder=\"0\" allow=\"autoplay; fullscreen; picture-in-picture; clipboard-write; encrypted-media; web-share\" referrerpolicy=\"strict-origin-when-cross-origin\" frameborder=\"0\" allow=\"autoplay; fullscreen; picture-in-picture\" data-ot-ignore><\/iframe>                <\/div>\n            \n            <!-- Block CTA -->\n            <div class=\"cta-block hidden\">\n                            <\/div>\n\n        <\/div>\n    <\/section>\n\n\n\n<p>La fatigue touche jusqu&#8217;\u00e0 80 % des personnes atteintes de CBP<sup>1<\/sup>, dont 20% la consid\u00e8rent comme importante ou alt\u00e9rant leur qualit\u00e9 de vie<sup>2<\/sup>. En tant que sympt\u00f4me distinct de la CBP, la fatigue peut consid\u00e9rablement alt\u00e9rer le fonctionnement quotidien, limiter l&#8217;activit\u00e9 physique et affecter le bien-\u00eatre \u00e9motionnel, ind\u00e9pendamment du prurit. Elle n\u00e9cessite donc une reconnaissance et une prise en charge sp\u00e9cifiques en tant que sympt\u00f4me distinct de la CBP.&nbsp;<\/p>\n\n\n\n<p><em>\u00ab\u202fIl est encourageant de constater l&#8217;\u00e9volution de la recherche, au point o\u00f9 l&#8217;on se demandent plus seulement si les personnes atteintes peuvent vivre longtemps avec leur maladie, mais plut\u00f4t si elles vivent r\u00e9ellement une bonne qualit\u00e9 de vie. \u00bb<\/em> \u2013 Mark Swain, h\u00e9patologue \u00e0 l&#8217;Universit\u00e9 de Calgary, au Canada&nbsp;<\/p>\n\n\n    <section class=\"video-card \">\n        <div class=\"container\">\n            <!-- Block Details -->\n            <div class=\"video-card-header\">\n                <h3 class=\"video-card-block-title hidden heading-three\">\n                                    <\/h3>\n                <p class=\"charcoal-grey video-card-block-summary hidden\"> \n                                    <\/p>\n            <\/div>\n\n            <!-- Video Iframe embed -->\n                            <div class=\"video-embed\"> \n                <iframe loading=\"lazy\" title=\"Video snippet 3\" src=\"https:\/\/player.vimeo.com\/video\/1112863007?app_id=122963&#038;autoplay=1&#038;muted=1&#038;controls=1&#038;loop=1&#038;autopause=1&#038;background=0\" width=\"640\" height=\"360\" frameborder=\"0\" allow=\"autoplay; fullscreen; picture-in-picture; clipboard-write; encrypted-media; web-share\" referrerpolicy=\"strict-origin-when-cross-origin\" frameborder=\"0\" allow=\"autoplay; fullscreen; picture-in-picture\" data-ot-ignore><\/iframe>                <\/div>\n            \n            <!-- Block CTA -->\n            <div class=\"cta-block hidden\">\n                            <\/div>\n\n        <\/div>\n    <\/section>\n\n\n\n<p>L&#8217;am\u00e9lioration des connaissances scientifiques sur les sympt\u00f4mes de la CBP et leur biologie a permis de reconna\u00eetre que la fatigue, autrefois simplement qualifi\u00e9e de \u00ab fatigue \u00bb, pourrait \u00eatre li\u00e9e \u00e0 une voie biologique. \u00c0 mesure que nous comprenons l&#8217;ensemble des sympt\u00f4mes et les m\u00e9canismes qui les sous-tendent, la prise en charge de la CBP peut devenir plus \u00e9clair\u00e9e et adapt\u00e9e \u00e0 des besoins sp\u00e9cifiques.\u00a0<\/p>\n\n\n    <section class=\"video-card \">\n        <div class=\"container\">\n            <!-- Block Details -->\n            <div class=\"video-card-header\">\n                <h3 class=\"video-card-block-title hidden heading-three\">\n                                    <\/h3>\n                <p class=\"charcoal-grey video-card-block-summary hidden\"> \n                                    <\/p>\n            <\/div>\n\n            <!-- Video Iframe embed -->\n                            <div class=\"video-embed\"> \n                <iframe loading=\"lazy\" title=\"Video snippet 4\" src=\"https:\/\/player.vimeo.com\/video\/1112863147?app_id=122963&#038;autoplay=1&#038;muted=1&#038;controls=1&#038;loop=1&#038;autopause=1&#038;background=0\" width=\"640\" height=\"360\" frameborder=\"0\" allow=\"autoplay; fullscreen; picture-in-picture; clipboard-write; encrypted-media; web-share\" referrerpolicy=\"strict-origin-when-cross-origin\" frameborder=\"0\" allow=\"autoplay; fullscreen; picture-in-picture\" data-ot-ignore><\/iframe>                <\/div>\n            \n            <!-- Block CTA -->\n            <div class=\"cta-block hidden\">\n                            <\/div>\n\n        <\/div>\n    <\/section>\n\n\n\n<p>Il est essentiel d&#8217;am\u00e9liorer la compr\u00e9hension de la CBP par les patients, et les professionnels de sant\u00e9 doivent prendre le temps d&#8217;expliquer les aspects cl\u00e9s de la maladie, comme le taux de phosphatases alcalines. Il est tout aussi important d&#8217;\u00e9couter attentivement et de valider le v\u00e9cu des personnes atteintes de CBP. Ensemble, ces actions aident les personnes atteintes de CBP \u00e0 se sentir plus autonomes et \u00e0 jouer un r\u00f4le actif dans leurs soins et \u00e0 collaborer avec leur \u00e9quipe soignante pour g\u00e9rer la CBP dont elles souffrent.\u00a0<\/p>\n\n\n\n<p>Notre compr\u00e9hension de l&#8217;h\u00e9t\u00e9rog\u00e9n\u00e9it\u00e9 de la CBP s&#8217;am\u00e9liore, et il est clair que la prise en charge n\u00e9cessite plus qu&#8217;une surveillance de routine. Elle exige une approche personnalis\u00e9e et holistique qui va au-del\u00e0 des r\u00e9sultats de laboratoire et se concentrer sur les sympt\u00f4mes les plus importants pour chaque personne atteinte de CBP.&nbsp;<\/p>\n\n\n\n<!--Alert Card Layout Start Here-->\n<section class=\"alertcard-section\">\n      <div class=\"container\">\n        <!--Alert Box HTML Start Here-->\n        <div class=\"alert-box general-box\">\n                  <div class=\"info-contents\">\n          <h4 role=\"heading\" aria-level=\"2\" class=\"info-head heading-four heading-four\">R\u00e9f\u00e9rences<\/h4>\n            <p class=\"info-sub-head-para hidden heading-para\"><\/p>\n            <div class=\"alert-content visible\"><ol>\n<li data-leveltext=\"%1.\" data-font=\"Rethink Sans\" data-listid=\"1\" data-list-defn-props=\"{&quot;335552541&quot;:0,&quot;335559685&quot;:720,&quot;335559991&quot;:360,&quot;469769242&quot;:[65533,0],&quot;469777803&quot;:&quot;left&quot;,&quot;469777804&quot;:&quot;%1.&quot;,&quot;469777815&quot;:&quot;hybridMultilevel&quot;}\" data-aria-posinset=\"1\" data-aria-level=\"1\"><span data-contrast=\"auto\">Faisal, A., 2024. Understanding fatigue and pruritus in primary biliary cholangitis.\u202fClinical Liver Disease,\u202f23;1, p.e0216.<\/span><span data-ccp-props=\"{&quot;201341983&quot;:0,&quot;335559740&quot;:259}\">\u00a0<\/span><\/li>\n<\/ol>\n<ol>\n<li data-leveltext=\"%1.\" data-font=\"Rethink Sans\" data-listid=\"1\" data-list-defn-props=\"{&quot;335552541&quot;:0,&quot;335559685&quot;:720,&quot;335559991&quot;:360,&quot;469769242&quot;:[65533,0],&quot;469777803&quot;:&quot;left&quot;,&quot;469777804&quot;:&quot;%1.&quot;,&quot;469777815&quot;:&quot;hybridMultilevel&quot;}\" data-aria-posinset=\"2\" data-aria-level=\"1\"><span data-contrast=\"auto\">Jopson, L. and Jones, D.E., 2015. Fatigue in primary biliary cirrhosis: prevalence, pathogenesis and management.\u202fDigestive Diseases,\u202f33(Suppl. 2), pp.109-114.<\/span><span data-ccp-props=\"{&quot;201341983&quot;:0,&quot;335559740&quot;:259}\">\u00a0<\/span><\/li>\n<\/ol>\n<\/div>\n          <\/div>\n        <\/div>\n        <!--Alert Box HTML Start Here-->\n      <\/div>\n    <\/section>\n<!--Alert Card Layout End Here-->\n","protected":false},"excerpt":{"rendered":"<p>Sandra Silvestri, d\u2019Ipsen, a rencontr\u00e9 le Dr Laura Cristoferi, le Professeur Mark Swain et le Professeur David Jones pour explorer<\/p>\n","protected":false},"author":97,"featured_media":85884,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_acf_changed":false,"_jetpack_memberships_contains_paid_content":false,"footnotes":""},"categories":[138],"tags":[],"class_list":["post-85888","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-rare-diseases","entry"],"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v26.8 - 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