{"id":61894,"date":"2024-07-24T12:11:34","date_gmt":"2024-07-24T10:11:34","guid":{"rendered":"https:\/\/www.ipsen.com\/?p=61894"},"modified":"2024-07-24T12:11:13","modified_gmt":"2024-07-24T10:11:13","slug":"les-manieres-dont-les-medecins-peuvent-contribuer-a-responsabiliser-les-personnes-atteintes-de-cholangite-biliaire-primitive","status":"publish","type":"post","link":"https:\/\/www.ipsen.com\/fr\/actualites\/rare-diseases-fr\/les-manieres-dont-les-medecins-peuvent-contribuer-a-responsabiliser-les-personnes-atteintes-de-cholangite-biliaire-primitive\/","title":{"rendered":"Les mani\u00e8res dont les m\u00e9decins peuvent contribuer \u00e0 responsabiliser les personnes atteintes de cholangite biliaire primitive\u00a0"},"content":{"rendered":"    <section class=\"video-card \">\n        <div class=\"container\">\n            <!-- Block Details -->\n            <div class=\"video-card-header\">\n                <h3 class=\"video-card-block-title hidden heading-three\">\n                                    <\/h3>\n                <p class=\"charcoal-grey video-card-block-summary hidden\"> \n                                    <\/p>\n            <\/div>\n\n            <!-- Video Iframe embed -->\n            \n            <!-- Block CTA -->\n            <div class=\"cta-block hidden\">\n                            <\/div>\n\n        <\/div>\n    <\/section>\n\n\n    <section class=\"video-card \">\n        <div class=\"container\">\n            <!-- Block Details -->\n            <div class=\"video-card-header\">\n                <h3 class=\"video-card-block-title hidden heading-three\">\n                                    <\/h3>\n                <p class=\"charcoal-grey video-card-block-summary hidden\"> \n                                    <\/p>\n            <\/div>\n\n            <!-- Video Iframe embed -->\n                            <div class=\"video-embed\"> \n                <iframe loading=\"lazy\" title=\"Comms_elafibranor_KOL Fireside Chat Full Video_June 2024\" src=\"https:\/\/player.vimeo.com\/video\/989023046?app_id=122963&#038;autoplay=1&#038;muted=1&#038;controls=1&#038;loop=1&#038;autopause=1&#038;background=0\" width=\"640\" height=\"360\" frameborder=\"0\" allow=\"autoplay; fullscreen; picture-in-picture; clipboard-write; encrypted-media; web-share\" referrerpolicy=\"strict-origin-when-cross-origin\" frameborder=\"0\" allow=\"autoplay; fullscreen; picture-in-picture\" data-ot-ignore><\/iframe>                <\/div>\n            \n            <!-- Block CTA -->\n            <div class=\"cta-block hidden\">\n                            <\/div>\n\n        <\/div>\n    <\/section>\n\n\n\n<p>Lors du congr\u00e8s de l\u2019Association europ\u00e9enne pour l\u2019\u00e9tude du foie (European Association for the Study of the Liver, EASL), d\u2019\u00e9minents sp\u00e9cialistes en h\u00e9patologie, Dr Mark Swain, Dr Emma Culver et Dr Marco Carbone ont \u00e9chang\u00e9 sur l\u2019efficacit\u00e9 de la prise en charge de la cholangite biliaire primitive (CBP). Les conversations ont abord\u00e9 les sujets tels que l\u2019importance des examens m\u00e9dicaux r\u00e9guliers, une approche visant des soins personnalis\u00e9s et la responsabilit\u00e9 partag\u00e9e de la prise en charge de la maladie entre les m\u00e9decins et les patients souffrant de CBP. \u202f&nbsp;<\/p>\n\n\n\n<p>La CBP est une maladie h\u00e9patique cholestatique auto-immune rare qui entra\u00eene des l\u00e9sions progressives, dont la pr\u00e9valence augmente dans le monde entier.<sup>1-4 <\/sup>La CBP peut provoquer une inflammation chronique des voies biliaires, entra\u00eenant une accumulation de bile et de toxines dans le foie (cholestase), conduisant \u00e0 des cicatrices du tissu h\u00e9patique (fibrose) et \u00e9ventuellement \u00e0 une une cirrhose. Sans traitement ou si la prise en charge est inappropri\u00e9e, la CBP peut \u00e9ventuellement entra\u00eener une insuffisance h\u00e9patique.<sup>5,6<\/sup>&nbsp;&nbsp;<\/p>\n\n\n\n<p>L\u2019importance d\u2019envisager une approche holistique des soins aux patients, pour g\u00e9rer \u00e0 la fois les sympt\u00f4mes et la progression de la maladie, a \u00e9t\u00e9 abord\u00e9e. Un consensus fut \u00e9tabli quant \u00e0 la n\u00e9cessit\u00e9 d\u2019informer les patients sur la pertinence des analyses biologiques h\u00e9patiques et de les aider \u00e0 comprendre l\u2019importance de la gestion des biomarqueurs de progression de la CBP, tels que le taux de phosphatases alcalines (PAL) et de bilirubine, pour faciliter la participation \u00e0 la prise en charge de leur maladie.&nbsp;&nbsp;<\/p>\n\n\n\n<p>Les sp\u00e9cialistes ont r\u00e9fl\u00e9chi \u00e0 la mani\u00e8re d\u2019atteindre l\u2019objectif g\u00e9n\u00e9ral d\u2019une consultation qui est de r\u00e9pondre totalement aux pr\u00e9occupations des patients. Les sympt\u00f4mes tels que la fatigue, les d\u00e9mangeaisons et la s\u00e9cheresse des yeux \/ de la bouche sont souvent peu reconnus et insuffisamment trait\u00e9s, bien qu\u2019ils aient un impact significatif sur la vie quotidienne des personnes atteintes de CBP. Il a \u00e9t\u00e9 soulign\u00e9 au cours des discussions qu\u2019il \u00e9tait important que les m\u00e9decins soient \u00e0 l\u2019\u00e9coute de l\u2019impact des sympt\u00f4mes sur la qualit\u00e9 de vie et qu\u2019ils r\u00e9agissent en leur prodiguant des conseils appropri\u00e9s.&nbsp;&nbsp;<\/p>\n\n\n\n<p>Il a \u00e9t\u00e9 convenu que les patients et leurs m\u00e9decins devaient se rencontrer r\u00e9guli\u00e8rement lors de consultations au moins tous les six \u00e0 douze mois. Lors de ces consultations, les patients doivent avoir la possibilit\u00e9 de discuter du statut de leur maladie en ce qui concerne les taux de PAL et de bilirubine, ainsi que de l\u2019impact de leurs sympt\u00f4mes sur leur qualit\u00e9 de vie.&nbsp;<\/p>\n\n\n\n<p>Il a \u00e9t\u00e9 conclu que les m\u00e9decins qui privil\u00e9gient une approche de prise en charge partag\u00e9e, qui \u00e9coutent les besoins des patients et les impliquent dans la prise de d\u00e9cision, contribuent \u00e0 donner aux patients les moyens de g\u00e9rer leur maladie.&nbsp;&nbsp;<\/p>\n\n\n\n<!--Alert Card Layout Start Here-->\n<section class=\"alertcard-section\">\n      <div class=\"container\">\n        <!--Alert Box HTML Start Here-->\n        <div class=\"alert-box general-box\">\n                    <div class=\"info-icon\">\n              <span class=\"info-circle\"><img decoding=\"async\" src=\"https:\/\/www.ipsen.com\/wp-content\/themes\/ipsen-main\/dist\/images\/alert-info-icon.png\" alt=\"Alert\"\/><\/i>\n            <\/div>\n                    <div class=\"info-contents\">\n          <h4 role=\"heading\" aria-level=\"2\" class=\"info-head heading-four heading-four\">R\u00e9f\u00e9rences<\/h4>\n            <p class=\"info-sub-head-para visible heading-para\"><\/p>\n            <div class=\"alert-content visible\"><ol>\n<li><em>Lv T, et al. J Gastroenterol Hepatol. 2021;36(6):1423\u20131434.\u00a0<\/em><\/li>\n<li><em>Galoosian A, et al. J Clin Transl Hepatol. 2020;8(1):49-60.\u00a0<\/em><\/li>\n<li><em>Lindor KD, et al. Hepatology. 2019;69(1):394-419.\u00a0<\/em><\/li>\n<li><em>Kumagi T &amp; Heathcote EJ. Orphanet J Rare Di. 2008;3:1.\u00a0<\/em><\/li>\n<li><em>Younossi ZM, et al. Am J Gastroenterol. 2019;114(1):48\u201363.\u00a0<\/em><\/li>\n<li><em>Hirschfield GM, et al. Expert Rev Gastroenterol Hepatol. 2021;15(8):929-939\u00a0<\/em><\/li>\n<\/ol>\n<\/div>\n          <\/div>\n        <\/div>\n        <!--Alert Box HTML Start Here-->\n      <\/div>\n    <\/section>\n<!--Alert Card Layout End Here-->\n","protected":false},"excerpt":{"rendered":"<p>Lors du congr\u00e8s de l\u2019Association europ\u00e9enne pour l\u2019\u00e9tude du foie (European Association for the Study of the Liver, EASL), d\u2019\u00e9minents<\/p>\n","protected":false},"author":11,"featured_media":61868,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_acf_changed":false,"_jetpack_memberships_contains_paid_content":false,"footnotes":""},"categories":[1192],"tags":[],"class_list":["post-61894","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-rare-diseases-fr","entry"],"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v26.8 - 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