{"id":34241,"date":"2023-07-07T09:10:31","date_gmt":"2023-07-07T07:10:31","guid":{"rendered":"https:\/\/www.ipsen.com\/?p=34241"},"modified":"2024-05-21T08:01:15","modified_gmt":"2024-05-21T06:01:15","slug":"la-cholangite-biliaire-primitive-cbp-regarder-au-dela-du-foie","status":"publish","type":"post","link":"https:\/\/www.ipsen.com\/fr\/actualites\/rare-diseases-fr\/la-cholangite-biliaire-primitive-cbp-regarder-au-dela-du-foie\/","title":{"rendered":"La cholangite biliaire primitive (CBP)\u202f: regarder au-del\u00e0 du foie"},"content":{"rendered":"    <section class=\"video-card \">\n        <div class=\"container\">\n            <!-- Block Details -->\n            <div class=\"video-card-header\">\n                <h3 class=\"video-card-block-title hidden heading-three\">\n                                    <\/h3>\n                <p class=\"charcoal-grey video-card-block-summary hidden\"> \n                                    <\/p>\n            <\/div>\n\n            <!-- Video Iframe embed -->\n                            <div class=\"video-embed\"> \n                <iframe loading=\"lazy\" title=\"Comms_Elafibranor_EASL KOL Thought Leadership Video_June 2023_V2\" src=\"https:\/\/player.vimeo.com\/video\/842875618?app_id=122963&#038;autoplay=1&#038;muted=1&#038;controls=1&#038;loop=1&#038;autopause=1&#038;background=0\" width=\"640\" height=\"360\" frameborder=\"0\" allow=\"autoplay; fullscreen; picture-in-picture; clipboard-write; encrypted-media; web-share\" referrerpolicy=\"strict-origin-when-cross-origin\" frameborder=\"0\" allow=\"autoplay; fullscreen; picture-in-picture\" data-ot-ignore><\/iframe>                <\/div>\n            \n            <!-- Block CTA -->\n            <div class=\"cta-block hidden\">\n                            <\/div>\n\n        <\/div>\n    <\/section>\n\n\n\n<p><strong><em>\u00ab\u202fVivre avec la charge symptomatique est la principale difficult\u00e9 pour le patient\u202f\u00bb \u2013 <\/em><\/strong>Professeur Andreas Kremer, h\u00e9patologue \u00e0 l&#8217;h\u00f4pital universitaire de Zurich.&nbsp;<\/p>\n\n\n\n<p>La cholangite biliaire primitive (CBP) est une maladie rare, chronique et auto-immune du foie. Elle peut avoir un impact significatif sur la qualit\u00e9 de vie d&#8217;une personne et, en l&#8217;absence de traitement, causer une insuffisance h\u00e9patique ou entra\u00eener la mort pr\u00e9matur\u00e9e<sup>1<\/sup>.&nbsp;<\/p>\n\n\n\n<p><strong><em>\u00ab\u202fUne chose que nous avons apprise de nos patients est qu&#8217;ils ont besoin d&#8217;\u00eatre \u00e9cout\u00e9s. Nous devons leur donner cette opportunit\u00e9 et les interroger constamment sur leurs sympt\u00f4mes\u202f\u00bb \u2013 <\/em><\/strong>Dr Cynthia Levy, h\u00e9patologue \u00e0 l&#8217;h\u00f4pital universitaire de Miami<strong><em>.<\/em><\/strong>&nbsp;<\/p>\n\n\n\n<p>Les personnes atteintes de CBP souffrent de sympt\u00f4mes comme les d\u00e9mangeaisons (prurit), la fatigue et la jaunisse<sup>2<\/sup> et courent de plus grands risques d&#8217;\u00eatre g\u00ean\u00e9es dans leur vie quotidienne, dans leur pratique d&#8217;un loisir ou d&#8217;un sport par exemple<sup>3 <\/sup>. Ce sont les d\u00e9mangeaisons et la fatigue, dont souffrent respectivement 70\u202f% et 90\u202f% des patients<sup>4<\/sup>, qui affectent le plus la qualit\u00e9 de vie. Les d\u00e9mangeaisons s\u00e9v\u00e8res peuvent affecter le sommeil, favoriser la d\u00e9pression et, dans certains cas, provoquer des pens\u00e9es suicidaires<sup>5<\/sup>.&nbsp;<\/p>\n\n\n\n<p><strong><em>\u00ab\u202fCertains patients nous font part de leurs craintes que les autres croient qu&#8217;ils sont atteints d&#8217;une maladie infectieuse contagieuse. Du coup ils ont peur et n&#8217;osent pas sortir en public et cette situation affecte \u00e0 la fois leur vie conjugale \u00e0 la maison et professionnelle en dehors\u202f\u00bb \u2013 <\/em><\/strong>Dr Cynthia Levy, h\u00e9patologue \u00e0 l&#8217;h\u00f4pital universitaire de Miami<strong><em>.<\/em><\/strong>&nbsp;<\/p>\n\n\n\n<p>Au cours du dernier congr\u00e8s annuel de l&#8217;Association europ\u00e9enne pour l&#8217;\u00e9tude du foie (AEEF), qui s&#8217;est tenu du 21 au 24 juin 2023 \u00e0 Vienne (Autriche), le docteur Cynthia Levy et le professeur Andreas Kremer ont pris le temps d&#8217;\u00e9couter des patients d\u00e9crire l&#8217;impact de la cholangite biliaire primaire sur leur quotidien et de discuter de l&#8217;\u00e9tat actuel de la lutte contre cette maladie. Ils ont aussi soulign\u00e9 l&#8217;importance de regarder au-del\u00e0 du foie pour am\u00e9liorer la qualit\u00e9 de vie.&nbsp;&nbsp;<\/p>\n\n\n\n<p><strong><em>\u00ab\u202fNous ne nous contentons pas de lutter contre la maladie h\u00e9patique, nous prenons aussi en charge toutes les manifestations extra-h\u00e9patiques que nous observons chez nos patients. Pour v\u00e9ritablement aborder la maladie sous l&#8217;angle de ces deux probl\u00e9matiques diff\u00e9rentes, nous devons optimiser, prendre en charge, traiter, dans la mesure du possible\u202f\u00bb \u2013 <\/em><\/strong>Professeur Andreas Kremer, h\u00e9patologue \u00e0 l&#8217;h\u00f4pital universitaire de Zurich<strong><em>.<\/em><\/strong>&nbsp;<\/p>\n\n\n\n<!--Alert Card Layout Start Here-->\n<section class=\"alertcard-section\">\n      <div class=\"container\">\n        <!--Alert Box HTML Start Here-->\n        <div class=\"alert-box info-box\">\n                    <div class=\"info-icon\">\n              <span class=\"info-circle\"><img decoding=\"async\" src=\"https:\/\/www.ipsen.com\/wp-content\/themes\/ipsen-main\/dist\/images\/alert-general-icon.png\" alt=\"Alert\"\/><\/i>\n            <\/div>\n                    <div class=\"info-contents\">\n          <h4 role=\"heading\" aria-level=\"2\" class=\"info-head heading-four heading-four\">R\u00e9f\u00e9rences\u202f:\u00a0<\/h4>\n            <p class=\"info-sub-head-para visible heading-para\"><\/p>\n            <div class=\"alert-content visible\"><ol>\n<li data-leveltext=\"%1.\" data-font=\"Calibri\" data-listid=\"1\" data-list-defn-props=\"{&quot;335552541&quot;:0,&quot;335559684&quot;:-1,&quot;335559685&quot;:720,&quot;335559991&quot;:360,&quot;469769242&quot;:[65533,0],&quot;469777803&quot;:&quot;left&quot;,&quot;469777804&quot;:&quot;%1.&quot;,&quot;469777815&quot;:&quot;hybridMultilevel&quot;}\" data-aria-posinset=\"1\" data-aria-level=\"1\"><span data-contrast=\"auto\">Younossi ZM, <\/span><i><span data-contrast=\"auto\">et al<\/span><\/i><span data-contrast=\"auto\">. 2019. Diagnosis and Management of Primary Biliary Cholangitis. <\/span><i><span data-contrast=\"auto\">Am J Gastroenterol<\/span><\/i><span data-contrast=\"auto\">. 114(1):48\u201363.<\/span><span data-ccp-props=\"{}\">\u00a0<\/span><\/li>\n<li data-leveltext=\"%1.\" data-font=\"Calibri\" data-listid=\"1\" data-list-defn-props=\"{&quot;335552541&quot;:0,&quot;335559684&quot;:-1,&quot;335559685&quot;:720,&quot;335559991&quot;:360,&quot;469769242&quot;:[65533,0],&quot;469777803&quot;:&quot;left&quot;,&quot;469777804&quot;:&quot;%1.&quot;,&quot;469777815&quot;:&quot;hybridMultilevel&quot;}\" data-aria-posinset=\"2\" data-aria-level=\"1\"><span data-contrast=\"none\">EASL. EASL Clinical Practice Guidelines: The diagnosis and management of patients with primary biliary cholangitis. <\/span><i><span data-contrast=\"none\">J Hepatol<\/span><\/i><span data-contrast=\"none\">. 2017;67(1):145\u2013172.<\/span><span data-ccp-props=\"{}\">\u00a0<\/span><\/li>\n<\/ol>\n<ol>\n<li data-leveltext=\"%1.\" data-font=\"Calibri\" data-listid=\"1\" data-list-defn-props=\"{&quot;335552541&quot;:0,&quot;335559684&quot;:-1,&quot;335559685&quot;:720,&quot;335559991&quot;:360,&quot;469769242&quot;:[65533,0],&quot;469777803&quot;:&quot;left&quot;,&quot;469777804&quot;:&quot;%1.&quot;,&quot;469777815&quot;:&quot;hybridMultilevel&quot;}\" data-aria-posinset=\"3\" data-aria-level=\"1\"><span data-contrast=\"none\">Selmi, C. <\/span><i><span data-contrast=\"none\">et al. <\/span><\/i><span data-contrast=\"none\">2007. Quality of life and everyday activities in patients with primary biliary cirrhosis.\u202f<\/span><i><span data-contrast=\"none\">Hepatology<\/span><\/i><span data-contrast=\"none\">,\u202f46(6), pp.1836-1843.<\/span><span data-ccp-props=\"{}\">\u00a0<\/span><\/li>\n<\/ol>\n<ol>\n<li data-leveltext=\"%1.\" data-font=\"Calibri\" data-listid=\"1\" data-list-defn-props=\"{&quot;335552541&quot;:0,&quot;335559684&quot;:-1,&quot;335559685&quot;:720,&quot;335559991&quot;:360,&quot;469769242&quot;:[65533,0],&quot;469777803&quot;:&quot;left&quot;,&quot;469777804&quot;:&quot;%1.&quot;,&quot;469777815&quot;:&quot;hybridMultilevel&quot;}\" data-aria-posinset=\"4\" data-aria-level=\"1\"><span data-contrast=\"auto\">C Levy <\/span><i><span data-contrast=\"auto\">et al.<\/span><\/i><span data-contrast=\"auto\"> 2023. Comprendre le v\u00e9cu des patients atteints de cholangite biliaire primitive et de prurit. Poster pr\u00e9sent\u00e9 au congr\u00e8s ISPOR, 7-11 mai 2023, Boston.<\/span><span data-ccp-props=\"{}\">\u00a0<\/span><\/li>\n<\/ol>\n<ol>\n<li data-leveltext=\"%1.\" data-font=\"Calibri\" data-listid=\"1\" data-list-defn-props=\"{&quot;335552541&quot;:0,&quot;335559684&quot;:-1,&quot;335559685&quot;:720,&quot;335559991&quot;:360,&quot;469769242&quot;:[65533,0],&quot;469777803&quot;:&quot;left&quot;,&quot;469777804&quot;:&quot;%1.&quot;,&quot;469777815&quot;:&quot;hybridMultilevel&quot;}\" data-aria-posinset=\"5\" data-aria-level=\"1\"><span data-contrast=\"none\">Gungabissoon, U. <\/span><i><span data-contrast=\"none\">et al.<\/span><\/i><span data-contrast=\"none\"> 2022. Disease burden of primary biliary cholangitis and associated pruritus based on a cross-sectional US claims analysis.\u202f<\/span><i><span data-contrast=\"none\">BMJ Open Gastroenterology<\/span><\/i><span data-contrast=\"none\">,\u202f9(1), p.e000857.<\/span><span data-ccp-props=\"{}\">\u00a0<\/span><\/li>\n<\/ol>\n<\/div>\n          <\/div>\n        <\/div>\n        <!--Alert Box HTML Start Here-->\n      <\/div>\n    <\/section>\n<!--Alert Card Layout End Here-->\n","protected":false},"excerpt":{"rendered":"<p>\u00ab\u202fVivre avec la charge symptomatique est la principale difficult\u00e9 pour le patient\u202f\u00bb \u2013 Professeur Andreas Kremer, h\u00e9patologue \u00e0 l&#8217;h\u00f4pital universitaire<\/p>\n","protected":false},"author":11,"featured_media":34255,"comment_status":"closed","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"_acf_changed":false,"_jetpack_memberships_contains_paid_content":false,"footnotes":""},"categories":[1192],"tags":[],"class_list":["post-34241","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-rare-diseases-fr","entry"],"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v26.8 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>La cholangite biliaire primitive (CBP)\u00a0: regarder au-del\u00e0 du foie | Ipsen Maladies Rares<\/title>\n<meta name=\"description\" content=\"Ipsen Maladies Rares ne se limite pas au foie dans la prise en charge de la cholangite biliaire primitive (CBP). 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