{"id":75423,"date":"2025-02-25T16:59:59","date_gmt":"2025-02-25T14:59:59","guid":{"rendered":"https:\/\/www.ipsen.com\/?page_id=75423"},"modified":"2026-04-07T16:35:30","modified_gmt":"2026-04-07T14:35:30","slug":"maladie-hepatique-cholestatique-rare","status":"publish","type":"page","link":"https:\/\/www.ipsen.com\/fr\/maladies-rares\/maladie-hepatique-cholestatique-rare\/","title":{"rendered":"Maladies cholestatiques rares"},"content":{"rendered":"    <section class=\"sub-page-banner \" style=\"background: linear-gradient(93.64deg, #224A81 2.99%, #2797D3 97.01%)\">\n        <div class=\"container content-sec\">\n            <nav aria-label=\"breadcrumb\">\n            <ol class=\"breadcrumb\">\n                <li class=\"breadcrumb-item\"><a href=\"https:\/\/www.ipsen.com\/fr\/\">Accueil<\/a><\/li><li class=\"breadcrumb-item visible\"><a href=\"https:\/\/www.ipsen.com\/fr\/science\/maladies-rares\/\">Maladies rares<\/a><\/li><li class=\"breadcrumb-item active\"><a class=\"link-pointer-events-none\" href=\"#\" aria-current=\"page\">Maladies cholestatiques rares<\/a><\/li><\/ol>\n            <\/nav>            <h1 class=\"visible\">Maladies cholestatiques rares<\/h1>\n            <p class=\"hidden\"><\/p>\n        <\/div>\n    <\/section>\n\n\n\n<section class=\"media-tabs\">\n      <div class=\"container\">\n        <div class=\"media-tabs-inner\">\n          <ul class=\"media-list-ul\">\n                              <li class=\"media-list-items\">\n                      <a class=\"media-item-link \" href=\"https:\/\/www.ipsen.com\/fr\/science\/maladies-rares\/\">Maladies rares<\/a>\n                  <\/li>\n                              <li class=\"media-list-items\">\n                      <a class=\"media-item-link active\" href=\"https:\/\/www.ipsen.com\/fr\/maladies-rares\/maladie-hepatique-cholestatique-rare\/\">Maladies cholestatiques rares<\/a>\n                  <\/li>\n                              <li class=\"media-list-items\">\n                      <a class=\"media-item-link \" href=\"https:\/\/www.ipsen.com\/fr\/maladies-rares\/maladies-osseuses-rares\/\">Maladies osseuses rares<\/a>\n                  <\/li>\n                              <li class=\"media-list-items\">\n                      <a class=\"media-item-link \" href=\"https:\/\/www.ipsen.com\/fr\/maladies-rares\/troubles-endocriniens-de-la-croissance\/\">Troubles endocriniens de la croissance<\/a>\n                  <\/li>\n                      <\/ul>\n          <div id=\"navTabArrows\">\n              <div class=\"tab-nav-arrows\" id=\"tab-nav-prev\"><\/div>\n              <div class=\"tab-nav-arrows\" id=\"tab-nav-next\"><\/div>\n          <\/div>\n        <\/div>\n      <\/div>\n<\/section>\n\n    <section class=\"title-text \">\n        <div class=\"container\">\n            <div class=\"title-text-inner\" style=\"background-color:#EDEBE4;\">\n\n                <!-- If heading is enabled then it's visible -->\n                <div class=\"text-head-dash hidden\">\n                <h3 class=\"heading-three\" role=\"heading\" aria-level=\"2\">\n                                            <\/h3>\n                <\/div>\n               \n                <!-- If description is enabled then it's visible -->\n                <div class=\"text-parbase visible\">\n                    <p>Les maladies cholestatiques rares du foie englobent un groupe de maladies rares qui affectent les voies biliaires, provoquant une maladie progressive du foie et des sympt\u00f4mes tels que des d\u00e9mangeaisons intenses et de la fatigue. Les sympt\u00f4mes peuvent \u00eatre gravement d\u00e9bilitants, mais ils sont souvent invisibles et incompris. La plupart des maladies cholestatiques rares du foie ne disposent que de traitements approuv\u00e9s limit\u00e9s. En raison de leur raret\u00e9, les patients doivent relever d&#8217;innombrables d\u00e9fis au quotidien. Le parcours vers le diagnostic peut \u00eatre long et tortueux. Les patients se sentent souvent isol\u00e9s et peu \u00e9cout\u00e9s. Ils se sentent parfois stigmatis\u00e9s et incompris. Le besoin d&#8217;innovation est \u00e9norme.<\/p>\n                <\/div>\n\n                <!-- If button is enabled then it's visible -->\n                \n            <\/div>\n        <\/div>\n    <\/section>\n\n\n<!--Graphics Cards Carousel Start Here-->\n\n    <section class=\"graphic-card graphics-old-layout bg-color-disabled bg-image-disabled bg-video-disabled bg-mobile-video-img-disabled\"    data-displaycards=\"2\">\n                <div class=\"container\">\n            <div class=\"text-graph-inner\">\n                <div class=\"row\">\n                    <!--Graphic info section-->\n                    <div class=\"column-1 col-xl-12 col-md-12 col-sm-12\">\n                        <div class=\"text-graph-heading\">\n                        <h3 class=\"charcoal-grey hidden heading-three\" role=\"heading\" aria-level=\"2\">\n                                                            <\/h3>\n                            <p class=\"text-graph-para charcoal-grey hidden\"><\/p>\n                        <\/div>\n                    <\/div><!--Graphic info section over here -->\n\n                    <!--Graphic detail section-->\n                    <div class=\"column-2 col-xl-12 col-md-12 col-sm-12\">\n                        <!-- graphic-card carousel start here -->\n                                                    <div class=\"text-graph-carousel\">\n                                <div class=\"glider-contain multiple\">\n                                                                                    <div class=\"text-graph-content-btn\">\n                                                    <button aria-hidden=\"true\" aria-label=\"Pr\u00e9c\u00e9dent\" class=\"glider-graphic-card-prev\"><span><\/span><\/button>\n                                                    <button aria-hidden=\"true\" aria-label=\"Suivant\" class=\"glider-graphic-card-next\"><span><\/span><\/button>\n                                                <\/div>\n                                    \n                                <div class=\"glider-graphic-card\" tabindex=\"-1\">\n                                                                                                                        <div class=\"text-graphic\">\n                                                    <div class=\"text-graph-row\">\n                                                        \n                                                                <!-- Graphic Card With OLD layout start here -->\n                                                                <div class=\"column-1\">\n                                                                                                                                                <div class=\"text-graph-img visible graphic-icon-enabled \">\n                                                                                                                                                                    <img decoding=\"async\" src=\"https:\/\/www.ipsen.com\/wp-content\/uploads\/2025\/07\/Medicine.png\" alt=\"\" \/> \n                                                                                                                                                            <\/div>\n                                                                                                                                    <\/div>\n                                                                <div class=\"column-2\">\n                                                                    <div class=\"text-graph-content\">\n                                                                                                                                                        <div class=\"text-graph-title\">\n                                                                                <h4 role=\"heading\" aria-level=\"3\">Le besoin d&#8217;innovation<\/h4>\n                                                                                <\/div>\n                                                                                                                                                <div class=\"text-graph-desc\">\n                                                                            <p><p>Il existe au moins 20 maladies h\u00e9patiques rares diff\u00e9rentes et chacune d&#8217;entre elles est unique.<\/p>\n<\/p>\n                                                                        <\/div>\n                                                                    <\/div>\n                                                                <\/div>\n                                                                <!-- Graphic Card With OLD layout end here -->\n                                                        \n                                                    <\/div>\n                                                <\/div>\n                                                                                                                                                                    <div class=\"text-graphic\">\n                                                    <div class=\"text-graph-row\">\n                                                        \n                                                                <!-- Graphic Card With OLD layout start here -->\n                                                                <div class=\"column-1\">\n                                                                                                                                                <div class=\"text-graph-img visible graphic-icon-enabled \">\n                                                                                                                                                                    <img decoding=\"async\" src=\"https:\/\/www.ipsen.com\/wp-content\/uploads\/2025\/07\/Rare-Disease-Common.png\" alt=\"\" \/> \n                                                                                                                                                            <\/div>\n                                                                                                                                    <\/div>\n                                                                <div class=\"column-2\">\n                                                                    <div class=\"text-graph-content\">\n                                                                                                                                                        <div class=\"text-graph-title\">\n                                                                                <h4 role=\"heading\" aria-level=\"3\">Rare atteinte du foie<\/h4>\n                                                                                <\/div>\n                                                                                                                                                <div class=\"text-graph-desc\">\n                                                                            <p><p>Les maladies h\u00e9patiques rares sont plus fr\u00e9quentes qu&#8217;on ne le pense, puisqu&#8217;elles touchent environ 1 personne sur 50 000 \u00e0 100 000.<\/p>\n<\/p>\n                                                                        <\/div>\n                                                                    <\/div>\n                                                                <\/div>\n                                                                <!-- Graphic Card With OLD layout end here -->\n                                                        \n                                                    <\/div>\n                                                <\/div>\n                                                                                                                                                                    <div class=\"text-graphic\">\n                                                    <div class=\"text-graph-row\">\n                                                        \n                                                                <!-- Graphic Card With OLD layout start here -->\n                                                                <div class=\"column-1\">\n                                                                                                                                                <div class=\"text-graph-img visible graphic-icon-enabled \">\n                                                                                                                                                                    <img decoding=\"async\" src=\"https:\/\/www.ipsen.com\/wp-content\/uploads\/2025\/07\/Question-Marks.png\" alt=\"\" \/> \n                                                                                                                                                            <\/div>\n                                                                                                                                    <\/div>\n                                                                <div class=\"column-2\">\n                                                                    <div class=\"text-graph-content\">\n                                                                                                                                                        <div class=\"text-graph-title\">\n                                                                                <h4 role=\"heading\" aria-level=\"3\">Des connaissances limit\u00e9es ou manquantes<\/h4>\n                                                                                <\/div>\n                                                                                                                                                <div class=\"text-graph-desc\">\n                                                                            <p><p>La plupart des professionnels de sant\u00e9 ont des connaissances limit\u00e9es en raison de la raret\u00e9 de ces maladies. Cela peut entra\u00eener un retard de diagnostic, les patients devant subir des examens et des rendez-vous fastidieux, et \u00eatre orient\u00e9s vers des sp\u00e9cialistes non n\u00e9cessaires dans le but de traiter les sympt\u00f4mes.<\/p>\n<\/p>\n                                                                        <\/div>\n                                                                    <\/div>\n                                                                <\/div>\n                                                                <!-- Graphic Card With OLD layout end here -->\n                                                        \n                                                    <\/div>\n                                                <\/div>\n                                                                                                                <\/div>\n                            <\/div>\n                                            <\/div> <!-- graphic-card carousel end here -->\n                <\/div> <!--Graphic detail section over here with 12 grid -->   \n            <\/div><!--row ended here-->\n        <\/div> <!-- graph-inner ended here -->\n        \n            <div class=\"more-result-btn\">\n                                            <\/div>\n        <\/div> <!--Container class ended here -->\n    <\/section>\n<!--Graphics Cards Carousel End Here-->\n\n\n<!-- Text & Media Block Code -->\n<section class=\"two-col-section text-media-section\">\n    <div class=\"container two-section-innner \">\n        <div class=\"response-inner\" style=\"background-image: url('')\">\n            <div class=\"row \">\n                <div class=\"col-xs-12 col-sm-12 col-md-6\">\n                                                    <div class=\"img-video-section\">\n                                <img decoding=\"async\" \n                                    src=\"https:\/\/www.ipsen.com\/wp-content\/uploads\/2025\/07\/cholestatic-2-1.jpg\" \n                                    alt=\"\" \n                                >\n                            <\/div>\n                                        <\/div>\n                <div class=\" col-xs-12 col-sm-12 col-md-6\">\n                    <div class=\"section-content\">\n                        <div class=\"heading-dash\">\n                                                            <span class=\"dash\"><\/span>\n                                <h4 class=\"heading-para heading-four\" role=\"heading\" aria-level=\"2\">\n                                    Cholangite biliaire primitive (CBP)                                <\/h4>\n                                                    <\/div>\n                                                <ul>\n<li>La CBP est une maladie auto-immune rare et progressive du foie, caract\u00e9ris\u00e9e par une accumulation de bile et de toxines (cholestase) et une inflammation chronique qui provoquent une fibrose (cicatrisation) irr\u00e9versible du foie et la destruction des voies biliaires.<\/li>\n<li>La CBP touche principalement les femmes entre 40 et 60 ans.<\/li>\n<li>La CBP est une maladie qui dure toute la vie et qui peut s&#8217;aggraver au fil du temps si elle n&#8217;est pas trait\u00e9e efficacement, ce qui peut entra\u00eener une greffe du foie et, dans certains cas, un d\u00e9c\u00e8s pr\u00e9matur\u00e9.<\/li>\n<li>La CBP affecte la vie quotidienne, les malades ressentant souvent des sympt\u00f4mes de fatigue s\u00e9v\u00e8re et des d\u00e9mangeaisons d\u00e9bilitantes (prurit).<\/li>\n<\/ul>\n                            <a \n                            aria-label=\" about Cholangite biliaire primitive (CBP)\"  \n                                role=\"link\" \n                                class=\"btn-link hidden\"\n                                href=\"\" \n                                target=\"_self\"\n                            > \n                                 \n                            <\/a>\n\n                    <\/div>\n                <\/div>\n            <\/div>\n        <\/div>\n    <\/div>\n<\/section>\n\n<!-- Text & Media Block Code -->\n<section class=\"two-col-section text-media-section\">\n    <div class=\"container two-section-innner section-reverse\">\n        <div class=\"response-inner\" style=\"background-image: url('')\">\n            <div class=\"row section-reverse\">\n                <div class=\"col-xs-12 col-sm-12 col-md-6\">\n                                                    <div class=\"img-video-section\">\n                                <img decoding=\"async\" \n                                    src=\"https:\/\/www.ipsen.com\/wp-content\/uploads\/2025\/07\/cholestatic-1-1.jpg\" \n                                    alt=\"\" \n                                >\n                            <\/div>\n                                        <\/div>\n                <div class=\" col-xs-12 col-sm-12 col-md-6\">\n                    <div class=\"section-content\">\n                        <div class=\"heading-dash\">\n                                                            <span class=\"dash\"><\/span>\n                                <h4 class=\"heading-para heading-four\" role=\"heading\" aria-level=\"2\">\n                                    Cholestase intrah\u00e9patique familiale progressive (PFIC)                                <\/h4>\n                                                    <\/div>\n                                                <ul>\n<li>La PFIC d\u00e9signe un ensemble de maladies g\u00e9n\u00e9tiques rares dans lesquelles le foie a du mal \u00e0 drainer l&#8217;acide biliaire, ce qui provoque une accumulation de bile dans le foie, connue sous le nom de cholestase intrah\u00e9patique.<\/li>\n<li>Bien que la PFIC puisse se manifester \u00e0 l&#8217;\u00e2ge adulte, c&#8217;est g\u00e9n\u00e9ralement chez les nourrissons et les jeunes enfants qu&#8217;elle se manifeste et qu&#8217;elle est la plus agressive.<\/li>\n<li>La PFIC peut \u00e9voluer rapidement et provoquer une cirrhose (cicatrisation \u00e0 long terme).<\/li>\n<li>Le sympt\u00f4me le plus invalidant de la PFIC est le prurit (d\u00e9mangeaisons intenses), qui peut \u00eatre si grave qu&#8217;il entra\u00eene une mutation de la peau, une perte de sommeil, de l&#8217;irritabilit\u00e9, une baisse de l&#8217;attention et une diminution des performances scolaires.<\/li>\n<\/ul>\n                            <a \n                            aria-label=\" about Cholestase intrah\u00e9patique familiale progressive (PFIC)\"  \n                                role=\"link\" \n                                class=\"btn-link hidden\"\n                                href=\"\" \n                                target=\"_self\"\n                            > \n                                 \n                            <\/a>\n\n                    <\/div>\n                <\/div>\n            <\/div>\n        <\/div>\n    <\/div>\n<\/section>\n\n<!-- Text & Media Block Code -->\n<section class=\"two-col-section text-media-section\">\n    <div class=\"container two-section-innner \">\n        <div class=\"response-inner\" style=\"background-image: url('')\">\n            <div class=\"row \">\n                <div class=\"col-xs-12 col-sm-12 col-md-6\">\n                                                    <div class=\"img-video-section\">\n                                <img decoding=\"async\" \n                                    src=\"https:\/\/www.ipsen.com\/wp-content\/uploads\/2025\/07\/cholestatic-4-1.jpg\" \n                                    alt=\"\" \n                                >\n                            <\/div>\n                                        <\/div>\n                <div class=\" col-xs-12 col-sm-12 col-md-6\">\n                    <div class=\"section-content\">\n                        <div class=\"heading-dash\">\n                                                            <span class=\"dash\"><\/span>\n                                <h4 class=\"heading-para heading-four\" role=\"heading\" aria-level=\"2\">\n                                    Syndrome d&#8217;Alagille (ALGS)                                <\/h4>\n                                                    <\/div>\n                                                <ul>\n<li>L&#8217;ALGS est une maladie g\u00e9n\u00e9tique rare du foie qui affecte principalement les b\u00e9b\u00e9s et les enfants en bas \u00e2ge, o\u00f9 les acides biliaires toxiques s&#8217;accumulent en raison du fait que les patients ont des canaux biliaires moins nombreux que la normale, r\u00e9tr\u00e9cis ou malform\u00e9s.<\/li>\n<li>L&#8217;ALGS peut affecter tous les organes du corps, y compris le foie, le c\u0153ur et les reins, et provoque des anomalies de la peau, du squelette et des yeux.<\/li>\n<li>L&#8217;un de ses principaux sympt\u00f4mes est un prurit intraitable, qui peut \u00eatre si grave qu&#8217;il conduit \u00e0 une greffe de foie.<\/li>\n<\/ul>\n                            <a \n                            aria-label=\" about Syndrome d'Alagille (ALGS)\"  \n                                role=\"link\" \n                                class=\"btn-link hidden\"\n                                href=\"\" \n                                target=\"_self\"\n                            > \n                                 \n                            <\/a>\n\n                    <\/div>\n                <\/div>\n            <\/div>\n        <\/div>\n    <\/div>\n<\/section>\n\n<!-- Text & Media Block Code -->\n<section class=\"two-col-section text-media-section\">\n    <div class=\"container two-section-innner section-reverse\">\n        <div class=\"response-inner\" style=\"background-image: url('')\">\n            <div class=\"row section-reverse\">\n                <div class=\"col-xs-12 col-sm-12 col-md-6\">\n                                                    <div class=\"img-video-section\">\n                                <img decoding=\"async\" \n                                    src=\"https:\/\/www.ipsen.com\/wp-content\/uploads\/2025\/07\/cholestatic-5-Edited.jpg\" \n                                    alt=\"\" \n                                >\n                            <\/div>\n                                        <\/div>\n                <div class=\" col-xs-12 col-sm-12 col-md-6\">\n                    <div class=\"section-content\">\n                        <div class=\"heading-dash\">\n                                                            <span class=\"dash\"><\/span>\n                                <h4 class=\"heading-para heading-four\" role=\"heading\" aria-level=\"2\">\n                                    Atr\u00e9sie des voies biliaires (BA)                                <\/h4>\n                                                    <\/div>\n                                                <ul>\n<li>La BA est une maladie qui touche les enfants lorsque les canaux biliaires \u00e0 l&#8217;ext\u00e9rieur et \u00e0 l&#8217;int\u00e9rieur du foie sont endommag\u00e9s et obstru\u00e9s.<\/li>\n<li>La bile ne pouvant s&#8217;\u00e9couler dans l&#8217;intestin, elle s&#8217;accumule dans le foie et l&#8217;endommage. Ces l\u00e9sions entra\u00eenent une cicatrisation, une perte de tissu et de fonction du foie et une cirrhose.<\/li>\n<\/ul>\n                            <a \n                            aria-label=\" about Atr\u00e9sie des voies biliaires (BA)\"  \n                                role=\"link\" \n                                class=\"btn-link hidden\"\n                                href=\"\" \n                                target=\"_self\"\n                            > \n                                 \n                            <\/a>\n\n                    <\/div>\n                <\/div>\n            <\/div>\n        <\/div>\n    <\/div>\n<\/section>\n\n<!-- Text & Media Block Code -->\n<section class=\"two-col-section text-media-section\">\n    <div class=\"container two-section-innner \">\n        <div class=\"response-inner\" style=\"background-image: url('')\">\n            <div class=\"row \">\n                <div class=\"col-xs-12 col-sm-12 col-md-6\">\n                                                    <div class=\"img-video-section\">\n                                <img decoding=\"async\" \n                                    src=\"https:\/\/www.ipsen.com\/wp-content\/uploads\/2025\/07\/cholestatic-3-1.jpg\" \n                                    alt=\"\" \n                                >\n                            <\/div>\n                                        <\/div>\n                <div class=\" col-xs-12 col-sm-12 col-md-6\">\n                    <div class=\"section-content\">\n                        <div class=\"heading-dash\">\n                                                            <span class=\"dash\"><\/span>\n                                <h4 class=\"heading-para heading-four\" role=\"heading\" aria-level=\"2\">\n                                    Cholangite scl\u00e9rosante primitive (CSP)                                <\/h4>\n                                                    <\/div>\n                                                <ul>\n<li>La CSP est une maladie rare du foie \u00e0 m\u00e9diation immunitaire dans laquelle l&#8217;inflammation et la fibrose entra\u00eenent le durcissement et le r\u00e9tr\u00e9cissement progressifs des canaux biliaires \u00e0 l&#8217;int\u00e9rieur et \u00e0 l&#8217;ext\u00e9rieur du foie.<\/li>\n<li>Les sympt\u00f4mes peuvent inclure des douleurs abdominales, des d\u00e9mangeaisons cutan\u00e9es, des diarrh\u00e9es, une jaunisse, de la fatigue et une sensation de faiblesse.<\/li>\n<li>De nombreux patients ne pr\u00e9sentent aucun sympt\u00f4me au moment du diagnostic de la CSP.<\/li>\n<li>Pour de nombreuses personnes, une greffe de foie est le seul traitement disponible lorsque la maladie a progress\u00e9 jusqu&#8217;\u00e0 l&#8217;insuffisance h\u00e9patique.<\/li>\n<\/ul>\n                            <a \n                            aria-label=\" about Cholangite scl\u00e9rosante primitive (CSP)\"  \n                                role=\"link\" \n                                class=\"btn-link hidden\"\n                                href=\"\" \n                                target=\"_self\"\n                            > \n                                 \n                            <\/a>\n\n                    <\/div>\n                <\/div>\n            <\/div>\n        <\/div>\n    <\/div>\n<\/section>\n\n\n<!--Regular card with carousel -->\n<section class=\"p-slider  bg-color-disabled \"  >\n      <div class=\"slider-heading-container\">\n          <h3 role=\"heading\" aria-level=\"2\" class=\"slider-title visible heading-three\">Actualit\u00e9s sur les maladies rares <\/h3>\n          <p class=\"charcoal-grey hidden\"><\/p>\n      <\/div>\n              \n            <!-- glider insert -->\n            <div class=\"glider-contain multiple\">\n                                    <!-- buttons -->\n                    <div class=\"slider-btns\">\n                    <button aria-label=\"Pr\u00e9c\u00e9dent\" aria-hidden=\"true\" tabindex=\"-1\" aria-labelledby=\"glider-product-prev\" role=\"button\" title=\"Pr\u00e9c\u00e9dent\" class=\"glider-product-prev\">\n                      <span style=\"background-image:url(https:\/\/www.ipsen.com\/wp-content\/themes\/ipsen-main\/dist\/images\/blue-left-arrow.png);\"><\/span>\n                    <\/button>\n                    <button aria-label=\"Suivant\" aria-hidden=\"true\" tabindex=\"-1\" aria-labelledby=\"glider-product-next\" role=\"button\" title=\"Suivant\" class=\"glider-product-next\">\n                      <span style=\"background-image:url(https:\/\/www.ipsen.com\/wp-content\/themes\/ipsen-main\/dist\/images\/blue-right-arrow.png);\"><\/span>\n                    <\/button>\n                <\/div>\n                                    <div class=\"glider-product\">\n                                                  <!-- product box-latest story listing-->\n                              <div class=\"product-box\" aria-label=\"\u00c9couter n\u2019est pas un slogan, c\u2019est le fondement de la prise en charge des maladies rares\">\n                              <a title=\"\u00c9couter n\u2019est pas un slogan, c\u2019est le fondement de la prise en charge des maladies rares\"  href=\"https:\/\/www.ipsen.com\/fr\/actualites\/rare-diseases-fr\/ecouter-nest-pas-un-slogan-cest-le-fondement-de-la-prise-en-charge-des-maladies-rares\/\">\n                                                                    <!-- img-container -->\n                                  <div class=\"p-img-container\">\n                                    <div class=\"p-img\">                                    \n                                    \n                                                                                      <img decoding=\"async\" src=\"https:\/\/www.ipsen.com\/wp-content\/uploads\/2026\/02\/Josep-Catlla-EVP-Corporate-Affairs-2026.jpg\" alt=\"\u00c9couter n\u2019est pas un slogan, c\u2019est le fondement de la prise en charge des maladies rares\" >\n                                                                                  \n                                    <\/div>\n                                  <\/div>\n                                  <!-- text-container -->\n                                                                    <div class=\"p-box-text\">\n                                                                                                                <button tabindex=\"-1\" class=\"btn-link card-btn visible\" style=\"background-color:#1e5ab2;\">\n                                            Maladies Rares                                        <\/button>\n                                                                                                                  <span class=\"time-stamp visible\">27 F\u00e9vrier 2026<\/span>\n                                                                            <span class=\"time-stamp visible\">3 \u00a0mn de lecture<\/span>\n                                                                            <div class=\"text-div\">\n                                       \n                                           <h4 role=\"heading\" aria-level=\"3\" class=\"text-div-para\">\u00c9couter n\u2019est pas un slogan, c\u2019est le fondement de la prise en charge des maladies rares<\/h4>\n                                          \n                                          <p>la Journ\u00e9e des maladies rares nous rappelle que ces pathologies touchent bien plus de personnes qu\u2019on ne l\u2019imagine : plus de 300 millions dans le monde, r\u00e9partis sur plus de 10 000 maladies rares identifi\u00e9es. Pourtant, ce qui me frappe le plus en cette journ\u00e9e de reconnaissance et de r\u00e9flexion, c\u2019est que l\u2019\u00e9coute des patients reste un levier encore sous\u2011exploit\u00e9 pour faire progresser les soins de sant\u00e9.<\/p>\n                                                                              <\/div>\n                                  <\/div>\n                                  <\/a>\n                                <\/div>\n                                                    <!-- product box-latest story listing-->\n                              <div class=\"product-box\" aria-label=\"Journ\u00e9e des maladies rares 2026 : \u00c9couter les patients pour imaginer de meilleurs futurs\">\n                              <a title=\"Journ\u00e9e des maladies rares 2026 : \u00c9couter les patients pour imaginer de meilleurs futurs\"  href=\"https:\/\/www.ipsen.com\/fr\/actualites\/rare-diseases-fr\/journee-des-maladies-rares-2026-ecouter-les-patients-pour-imaginer-de-meilleurs-futurs\/\">\n                                                                    <!-- img-container -->\n                                  <div class=\"p-img-container\">\n                                    <div class=\"p-img\">                                    \n                                    \n                                                                                      <img decoding=\"async\" src=\"https:\/\/www.ipsen.com\/wp-content\/uploads\/2026\/02\/RDD_0a83d2.jpg\" alt=\"Journ\u00e9e des maladies rares 2026 : \u00c9couter les patients pour imaginer de meilleurs futurs\" >\n                                                                                  \n                                    <\/div>\n                                  <\/div>\n                                  <!-- text-container -->\n                                                                    <div class=\"p-box-text\">\n                                                                                                                <button tabindex=\"-1\" class=\"btn-link card-btn visible\" style=\"background-color:#1e5ab2;\">\n                                            Maladies Rares                                        <\/button>\n                                                                                                                  <span class=\"time-stamp visible\">18 F\u00e9vrier 2026<\/span>\n                                                                            <span class=\"time-stamp visible\">3 \u00a0mn de lecture<\/span>\n                                                                            <div class=\"text-div\">\n                                       \n                                           <h4 role=\"heading\" aria-level=\"3\" class=\"text-div-para\">Journ\u00e9e des maladies rares 2026 : \u00c9couter les patients pour imaginer de meilleurs futurs<\/h4>\n                                          \n                                          <p>Les maladies rares sont plus r\u00e9pandues qu\u2019on ne le pense, tant par le nombre de vies qu\u2019elles touchent que par l\u2019impact profond qu\u2019elles ont sur le quotidien des patients et de leurs familles. Derri\u00e8re chaque diagnostic se trouve une personne qui affronte bien plus que des sympt\u00f4mes : une routine quotidienne boulevers\u00e9e, des projets de vie r\u00e9orient\u00e9s, l\u2019incompr\u00e9hension et l\u2019isolement \u00e0 surmonter, et des familles qui s\u2019adaptent \u00e0 l\u2019incertitude avec r\u00e9silience et espoir.<\/p>\n                                                                              <\/div>\n                                  <\/div>\n                                  <\/a>\n                                <\/div>\n                                                    <!-- product box-latest story listing-->\n                              <div class=\"product-box\" aria-label=\"Journ\u00e9e Mondiale du Syndrome d&#8217;Alagille &#8211; L\u00e0 o\u00f9 des connexions puissantes peuvent faire la diff\u00e9rence\">\n                              <a title=\"Journ\u00e9e Mondiale du Syndrome d&#8217;Alagille &#8211; L\u00e0 o\u00f9 des connexions puissantes peuvent faire la diff\u00e9rence\"  href=\"https:\/\/www.ipsen.com\/fr\/actualites\/rare-diseases-fr\/journee-mondiale-du-syndrome-dalagille-la-ou-des-connexions-puissantes-peuvent-faire-la-difference\/\">\n                                                                    <!-- img-container -->\n                                  <div class=\"p-img-container\">\n                                    <div class=\"p-img\">                                    \n                                    \n                                                                                      <img decoding=\"async\" src=\"https:\/\/www.ipsen.com\/wp-content\/uploads\/2026\/01\/Image1-2.jpg\" alt=\"Journ\u00e9e Mondiale du Syndrome d&#8217;Alagille &#8211; L\u00e0 o\u00f9 des connexions puissantes peuvent faire la diff\u00e9rence\" >\n                                                                                  \n                                    <\/div>\n                                  <\/div>\n                                  <!-- text-container -->\n                                                                    <div class=\"p-box-text\">\n                                                                                                                <button tabindex=\"-1\" class=\"btn-link card-btn visible\" style=\"background-color:#1e5ab2;\">\n                                            Maladies Rares                                        <\/button>\n                                                                                                                  <span class=\"time-stamp visible\">19 Janvier 2026<\/span>\n                                                                            <span class=\"time-stamp visible\">1 \u00a0mn de lecture<\/span>\n                                                                            <div class=\"text-div\">\n                                       \n                                           <h4 role=\"heading\" aria-level=\"3\" class=\"text-div-para\">Journ\u00e9e Mondiale du Syndrome d&#8217;Alagille &#8211; L\u00e0 o\u00f9 des connexions puissantes peuvent faire la diff\u00e9rence<\/h4>\n                                          \n                                          <p>Chez Ipsen, nous nous tenons aux c\u00f4t\u00e9s de l\u2019Alagille Syndrome Alliance le 24 janvier, Journ\u00e9e de sensibilisation \u00e0 l\u2019ALGS, et chaque jour. Nous comprenons l\u2019importance de soutenir les associations de patients dans leurs efforts pour sensibiliser \u00e0 ces maladies rares et complexes, afin que les familles sachent qu\u2019elles ne sont pas seules.<\/p>\n                                                                              <\/div>\n                                  <\/div>\n                                  <\/a>\n                                <\/div>\n                                                    <!-- product box-latest story listing-->\n                              <div class=\"product-box\" aria-label=\"This My PBC\">\n                              <a title=\"This My PBC\"  href=\"https:\/\/www.ipsen.com\/fr\/actualites\/rare-diseases-fr\/this-my-pbc\/\">\n                                                                    <!-- img-container -->\n                                  <div class=\"p-img-container\">\n                                    <div class=\"p-img\">                                    \n                                    \n                                                                                      <img decoding=\"async\" src=\"https:\/\/www.ipsen.com\/wp-content\/uploads\/2025\/11\/TiMPBC-Logo-Blue-scaled-1.png\" alt=\"This My PBC\" >\n                                                                                  \n                                    <\/div>\n                                  <\/div>\n                                  <!-- text-container -->\n                                                                    <div class=\"p-box-text\">\n                                                                                                                <button tabindex=\"-1\" class=\"btn-link card-btn visible\" style=\"background-color:#1e5ab2;\">\n                                            Maladies Rares                                        <\/button>\n                                                                                                                  <span class=\"time-stamp visible\">27 Novembre 2025<\/span>\n                                                                            <span class=\"time-stamp visible\">0 \u00a0mn de lecture<\/span>\n                                                                            <div class=\"text-div\">\n                                       \n                                           <h4 role=\"heading\" aria-level=\"3\" class=\"text-div-para\">This My PBC<\/h4>\n                                          \n                                          <p>\u201cThis is My PBC\u201d\u00a0est une initiative de sensibilisation \u00e0 la maladie, d\u00e9velopp\u00e9e et financ\u00e9e par Ipsen, qui vise \u00e0 mieux faire conna\u00eetre la cholangite biliaire primitive (PBC) et \u00e0 encourager les personnes vivant avec cette maladie \u00e0 en apprendre davantage sur leur condition. Elle souligne que chaque exp\u00e9rience est diff\u00e9rente et l\u00e9gitime.<\/p>\n                                                                              <\/div>\n                                  <\/div>\n                                  <\/a>\n                                <\/div>\n                                                    <!-- product box-latest story listing-->\n                              <div class=\"product-box\" aria-label=\"Rencontrez Jo, qui vit avec la CBP\">\n                              <a title=\"Rencontrez Jo, qui vit avec la CBP\"  href=\"https:\/\/www.ipsen.com\/fr\/actualites\/rare-diseases-fr\/rencontrez-jo-qui-vit-avec-la-cbp\/\">\n                                                                    <!-- img-container -->\n                                  <div class=\"p-img-container\">\n                                    <div class=\"p-img\">                                    \n                                    \n                                                                                      <img decoding=\"async\" src=\"https:\/\/www.ipsen.com\/wp-content\/uploads\/2025\/11\/TiMPBC_Webiste-Images_700x420_Jo.jpg\" alt=\"Rencontrez Jo, qui vit avec la CBP\" >\n                                                                                  \n                                    <\/div>\n                                  <\/div>\n                                  <!-- text-container -->\n                                                                    <div class=\"p-box-text\">\n                                                                                                                <button tabindex=\"-1\" class=\"btn-link card-btn visible\" style=\"background-color:#1e5ab2;\">\n                                            Maladies Rares                                        <\/button>\n                                                                                                                  <span class=\"time-stamp visible\">25 Novembre 2025<\/span>\n                                                                            <span class=\"time-stamp visible\">0 \u00a0mn de lecture<\/span>\n                                                                            <div class=\"text-div\">\n                                       \n                                           <h4 role=\"heading\" aria-level=\"3\" class=\"text-div-para\">Rencontrez Jo, qui vit avec la CBP<\/h4>\n                                          \n                                          <p>Le parcours de Jo a commenc\u00e9 il y a environ dix ans, lorsqu\u2019elle a consult\u00e9 son m\u00e9decin g\u00e9n\u00e9raliste en raison d\u2019une grande fatigue et d\u2019un \u00e9puisement g\u00e9n\u00e9ral. Ce n\u2019est qu\u2019il y a quatre ans, apr\u00e8s des analyses sanguines de routine et une biopsie du foie, qu\u2019elle a re\u00e7u son diagnostic. Les groupes de soutien, comme la PBC Foundation, ont \u00e9t\u00e9 une v\u00e9ritable r\u00e9v\u00e9lation pour Jo, lui offrant un accompagnement, des ressources \u00e9ducatives et une communaut\u00e9 partageant les m\u00eames exp\u00e9riences.<\/p>\n                                                                              <\/div>\n                                  <\/div>\n                                  <\/a>\n                                <\/div>\n                                                    <!-- product box-latest story listing-->\n                              <div class=\"product-box\" aria-label=\"Rencontrez Wendy, qui vit avec la CBP\">\n                              <a title=\"Rencontrez Wendy, qui vit avec la CBP\"  href=\"https:\/\/www.ipsen.com\/fr\/actualites\/rare-diseases-fr\/rencontrez-wendy-qui-vit-avec-la-cbp\/\">\n                                                                    <!-- img-container -->\n                                  <div class=\"p-img-container\">\n                                    <div class=\"p-img\">                                    \n                                    \n                                                                                      <img decoding=\"async\" src=\"https:\/\/www.ipsen.com\/wp-content\/uploads\/2025\/11\/TiMPBC_Webiste-Images_700x420_Wendy.jpg\" alt=\"Rencontrez Wendy, qui vit avec la CBP\" >\n                                                                                  \n                                    <\/div>\n                                  <\/div>\n                                  <!-- text-container -->\n                                                                    <div class=\"p-box-text\">\n                                                                                                                <button tabindex=\"-1\" class=\"btn-link card-btn visible\" style=\"background-color:#1e5ab2;\">\n                                            Maladies Rares                                        <\/button>\n                                                                                                                  <span class=\"time-stamp visible\">25 Novembre 2025<\/span>\n                                                                            <span class=\"time-stamp visible\">0 \u00a0mn de lecture<\/span>\n                                                                            <div class=\"text-div\">\n                                       \n                                           <h4 role=\"heading\" aria-level=\"3\" class=\"text-div-para\">Rencontrez Wendy, qui vit avec la CBP<\/h4>\n                                          \n                                          <p>Il lui a fallu cinq ann\u00e9es de consultations chez son m\u00e9decin g\u00e9n\u00e9raliste et chez des sp\u00e9cialistes avant d\u2019obtenir un diagnostic. Son conseil aux personnes vivant avec la CBP: allez chez votre m\u00e9decin en \u00e9tant bien pr\u00e9par\u00e9(e), posez beaucoup de questions, g\u00e9rez votre maladie du mieux possible et soyez bienveillant(e) envers vous-m\u00eame.<\/p>\n                                                                              <\/div>\n                                  <\/div>\n                                  <\/a>\n                                <\/div>\n                                                    <!-- product box-latest story listing-->\n                              <div class=\"product-box\" aria-label=\"Rencontrez Gill, qui vit avec la CBP\">\n                              <a title=\"Rencontrez Gill, qui vit avec la CBP\"  href=\"https:\/\/www.ipsen.com\/fr\/actualites\/rare-diseases-fr\/rencontrez-gill-qui-vit-avec-la-cbp\/\">\n                                                                    <!-- img-container -->\n                                  <div class=\"p-img-container\">\n                                    <div class=\"p-img\">                                    \n                                    \n                                                                                      <img decoding=\"async\" src=\"https:\/\/www.ipsen.com\/wp-content\/uploads\/2025\/11\/TiMPBC_Webiste-Images_700x420_Gill.jpg\" alt=\"Rencontrez Gill, qui vit avec la CBP\" >\n                                                                                  \n                                    <\/div>\n                                  <\/div>\n                                  <!-- text-container -->\n                                                                    <div class=\"p-box-text\">\n                                                                                                                <button tabindex=\"-1\" class=\"btn-link card-btn visible\" style=\"background-color:#1e5ab2;\">\n                                            Maladies Rares                                        <\/button>\n                                                                                                                  <span class=\"time-stamp visible\">25 Novembre 2025<\/span>\n                                                                            <span class=\"time-stamp visible\">0 \u00a0mn de lecture<\/span>\n                                                                            <div class=\"text-div\">\n                                       \n                                           <h4 role=\"heading\" aria-level=\"3\" class=\"text-div-para\">Rencontrez Gill, qui vit avec la CBP<\/h4>\n                                          \n                                          <p>Gill est une m\u00e8re et une grand-m\u00e8re d\u00e9vou\u00e9e, qui aime passer du temps avec ses petits-enfants et jardiner. Elle est \u00e9galement passionn\u00e9e par son travail de b\u00e9n\u00e9vole. Gill vit avec la CBP depuis plus de 20 ans.<\/p>\n                                                                              <\/div>\n                                  <\/div>\n                                  <\/a>\n                                <\/div>\n                                                    <!-- product box-latest story listing-->\n                              <div class=\"product-box\" aria-label=\"Ipsen au Liver Meeting 2025\">\n                              <a title=\"Ipsen au Liver Meeting 2025\"  href=\"https:\/\/www.ipsen.com\/fr\/actualites\/rare-diseases-fr\/ipsen-au-liver-meeting-2025\/\">\n                                                                    <!-- img-container -->\n                                  <div class=\"p-img-container\">\n                                    <div class=\"p-img\">                                    \n                                    \n                                                                                      <img decoding=\"async\" src=\"https:\/\/www.ipsen.com\/wp-content\/uploads\/2025\/10\/AASLD-Thumbnail.jpg\" alt=\"Ipsen au Liver Meeting 2025\" >\n                                                                                  \n                                    <\/div>\n                                  <\/div>\n                                  <!-- text-container -->\n                                                                    <div class=\"p-box-text\">\n                                                                                                                <button tabindex=\"-1\" class=\"btn-link card-btn visible\" style=\"background-color:#1e5ab2;\">\n                                            Maladies Rares                                        <\/button>\n                                                                                                                  <span class=\"time-stamp visible\">30 Octobre 2025<\/span>\n                                                                            <span class=\"time-stamp visible\">1 \u00a0mn de lecture<\/span>\n                                                                            <div class=\"text-div\">\n                                       \n                                           <h4 role=\"heading\" aria-level=\"3\" class=\"text-div-para\">Ipsen au Liver Meeting 2025<\/h4>\n                                          \n                                          <p>Nous sommes fiers de participer au Liver Meeting 2025 organis\u00e9 par l&#8217;American Association for the Study of Liver Disease (AASLD), o\u00f9 des professionnels de la sant\u00e9, des scientifiques et la communaut\u00e9 des patients se r\u00e9unissent pour discuter des derni\u00e8res avanc\u00e9es en mati\u00e8re d&#8217;innovations et de soins<\/p>\n                                                                              <\/div>\n                                  <\/div>\n                                  <\/a>\n                                <\/div>\n                                                    <!-- product box-latest story listing-->\n                              <div class=\"product-box\" aria-label=\"Le paysage en \u00e9volution des maladies du foie : innovation, int\u00e9gration et impact\">\n                              <a title=\"Le paysage en \u00e9volution des maladies du foie : innovation, int\u00e9gration et impact\"  href=\"https:\/\/www.ipsen.com\/fr\/actualites\/general-fr\/le-paysage-en-evolution-des-maladies-du-foie-innovation-integration-et-impact\/\">\n                                                                    <!-- img-container -->\n                                  <div class=\"p-img-container\">\n                                    <div class=\"p-img\">                                    \n                                    \n                                                                                      <img decoding=\"async\" src=\"https:\/\/www.ipsen.com\/wp-content\/uploads\/2025\/10\/IMG_6401-1.jpg\" alt=\"Le paysage en \u00e9volution des maladies du foie : innovation, int\u00e9gration et impact\" >\n                                                                                  \n                                    <\/div>\n                                  <\/div>\n                                  <!-- text-container -->\n                                                                    <div class=\"p-box-text\">\n                                                                                                                <button tabindex=\"-1\" class=\"btn-link card-btn visible\" style=\"background-color:#153f99;\">\n                                            G\u00e9n\u00e9ral                                        <\/button>\n                                                                                                                  <span class=\"time-stamp visible\">30 Octobre 2025<\/span>\n                                                                            <span class=\"time-stamp visible\">6 \u00a0mn de lecture<\/span>\n                                                                            <div class=\"text-div\">\n                                       \n                                           <h4 role=\"heading\" aria-level=\"3\" class=\"text-div-para\">Le paysage en \u00e9volution des maladies du foie : innovation, int\u00e9gration et impact<\/h4>\n                                          \n                                          <p>Les maladies du foie sont devenues un domaine d\u2019int\u00e9r\u00eat majeur pour la communaut\u00e9 scientifique m\u00e9dicale, en raison de besoins non satisfaits importants \u2014 notamment dans les pathologies rares et peu prises en charge. <\/p>\n                                                                              <\/div>\n                                  <\/div>\n                                  <\/a>\n                                <\/div>\n                                                    <!-- product box-latest story listing-->\n                              <div class=\"product-box\" aria-label=\"Journ\u00e9e de sensibilisation \u00e0 la CBP\u00a0: Confronter les pr\u00e9jug\u00e9s et faire entendre la voix des patients\">\n                              <a title=\"Journ\u00e9e de sensibilisation \u00e0 la CBP\u00a0: Confronter les pr\u00e9jug\u00e9s et faire entendre la voix des patients\"  href=\"https:\/\/www.ipsen.com\/fr\/actualites\/rare-diseases-fr\/journee-de-sensibilisation-a-la-cbp-confronter-les-prejuges-et-faire-entendre-la-voix-des-patients\/\">\n                                                                    <!-- img-container -->\n                                  <div class=\"p-img-container\">\n                                    <div class=\"p-img\">                                    \n                                    \n                                                                                      <img decoding=\"async\" src=\"https:\/\/www.ipsen.com\/wp-content\/uploads\/2025\/09\/Ipsen.com-article-Picture.jpg\" alt=\"Journ\u00e9e de sensibilisation \u00e0 la CBP\u00a0: Confronter les pr\u00e9jug\u00e9s et faire entendre la voix des patients\" >\n                                                                                  \n                                    <\/div>\n                                  <\/div>\n                                  <!-- text-container -->\n                                                                    <div class=\"p-box-text\">\n                                                                                                                <button tabindex=\"-1\" class=\"btn-link card-btn visible\" style=\"background-color:#1e5ab2;\">\n                                            Maladies Rares                                        <\/button>\n                                                                                                                  <span class=\"time-stamp visible\">18 Septembre 2025<\/span>\n                                                                            <span class=\"time-stamp visible\">3 \u00a0mn de lecture<\/span>\n                                                                            <div class=\"text-div\">\n                                       \n                                           <h4 role=\"heading\" aria-level=\"3\" class=\"text-div-para\">Journ\u00e9e de sensibilisation \u00e0 la CBP\u00a0: Confronter les pr\u00e9jug\u00e9s et faire entendre la voix des patients<\/h4>\n                                          \n                                          <p>Pour les milliers de personnes, principalement des femmes, atteintes de cholangite biliaire primitive (CBP), une maladie h\u00e9patique auto-immune chronique et \u00e9volutive, le parcours peut \u00eatre solitaire.<\/p>\n                                                                              <\/div>\n                                  <\/div>\n                                  <\/a>\n                                <\/div>\n                                        <\/div>\n            <\/div>\n           \n      <div class=\"cta-block hidden\">\n                <\/div>\n  <\/section>\n","protected":false},"excerpt":{"rendered":"","protected":false},"author":11,"featured_media":0,"parent":91221,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"_acf_changed":false,"footnotes":""},"class_list":["post-75423","page","type-page","status-publish","hentry","entry"],"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v26.8 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Maladies cholestatiques rares - Global<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link 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